Auditory function in individuals within Leber's hereditary optic neuropathy pedigrees

Journal of Neurology

Volumn 259, Issue 3, 2012, Pages 542-550

  Rance, Gary ^a   Kearns, Lisa S ^a   Tan, Johanna ^a   Gravina, Anthony ^a   Rosenfeld, Lisa ^a   Henley, Lauren ^a   Carew, Peter ^a   Graydon, Kelley ^a   O'Hare, Fleur ^a   Mack, David A ^b,c  

^a UNIVERSITY OF MELBOURNE   (Australia)

^b ROYAL VICTORIAN EYE AND EAR HOSPITAL   (Australia)

^c UNIVERSITY OF WESTERN AUSTRALIA   (Australia)

Author keywords

Auditory neuropathy; Leber's; LHON; Speech perception; Temporal processing

Indexed keywords

MITOCHONDRIAL DNA;

ADOLESCENT; ADULT; ARTICLE; ASYMPTOMATIC DISEASE; CHILD; CLINICAL ARTICLE; COHORT ANALYSIS; CONTROLLED STUDY; EVOKED BRAIN STEM AUDITORY RESPONSE; FEMALE; GENE MUTATION; GENETIC SCREENING; HEARING DISORDER; HUMAN; LEBER HEREDITARY OPTIC NEUROPATHY; MALE; NERVOUS SYSTEM ELECTROPHYSIOLOGY; NOISE; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; SOUND DETECTION; SPEECH PERCEPTION; VESTIBULOCOCHLEAR NERVE DISEASE; VISUAL IMPAIRMENT;

ACOUSTIC STIMULATION; ADOLESCENT; ADULT; AGE FACTORS; CHILD; COHORT STUDIES; DNA, MITOCHONDRIAL; ELECTROENCEPHALOGRAPHY; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; FEMALE; HEARING LOSS, CENTRAL; HUMANS; MALE; OPTIC ATROPHY, HEREDITARY, LEBER; PEDIGREE; POINT MUTATION; PSYCHOACOUSTICS; REACTION TIME; SPEECH PERCEPTION; VISUAL ACUITY; YOUNG ADULT;

EID: 84860609326     PISSN: 03405354     EISSN: 14321459     Source Type: Journal    
DOI: 10.1007/s00415-011-6230-7     Document Type: Article

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