Successful treatment of auditory perceptual disorder in individuals with Friedreich ataxia

Neuroscience

Volumn 171, Issue 2, 2010, Pages 552-555

  Rance, G ^a   Corben, L A ^b   Du Bourg, E ^a   King, A ^c   Delatycki, M B ^b  

^a UNIVERSITY OF MELBOURNE   (Australia)

^b Bruce Lefroy Centre for Genetic Health Research   (Australia)

^c Australian Hearing   (Australia)

Author keywords

Auditory neuropathy; Auditory processing; Friedreich ataxia; Speech perception

Indexed keywords

ADOLESCENT; ADULT; AMPLITUDE MODULATION; ARTICLE; AUDITORY DISCRIMINATION; AUDITORY MASKING; AUDITORY REHABILITATION; AUDITORY SYSTEM FUNCTION; BRAIN FUNCTION; CHILD; CLINICAL ARTICLE; COHORT ANALYSIS; COMMUNICATION DISORDER; CONTROLLED STUDY; EVOKED BRAIN STEM AUDITORY RESPONSE; FEMALE; FRIEDREICH ATAXIA; HEARING TEST; HUMAN; MALE; NOISE; PERCEPTION DEAFNESS; PRIORITY JOURNAL; SCHOOL CHILD; SPEECH PERCEPTION; TELECOMMUNICATION; VESTIBULOCOCHLEAR NERVE DISEASE;

ADOLESCENT; ADULT; AUDITORY PERCEPTUAL DISORDERS; CHILD; FEMALE; FRIEDREICH ATAXIA; HEARING AIDS; HEARING TESTS; HUMANS; MALE; SPEECH PERCEPTION; YOUNG ADULT;

EID: 78149285630     PISSN: 03064522     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neuroscience.2010.09.013     Document Type: Article

References (12)

1. Campuzano V., Montermini L., Molto D., et al. Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion. Science 1996, 271:1423-1427.
2. Cossee M., Durr A., Schmitt M., et al. Friedreich's ataxia: point mutations and clinical presentations of compound heterozygotes. Ann Neurol 1999, 45:200-206.
3. Hawkins D. Comparisons of speech recognition in noise by mildly-to moderately-hearing-impaired children using hearing aids and FM systems. J Speech Hear Disord 1984, 49:409-418.
4. Johnstone K.N., John A.B., Hall J.W., Crandell C.C. Multiple benefits of personal FM system use by children with auditory processing disorder (APD). Int J Audiol 2009, 48:371-383.
5. Peterson G., Lehiste I. Revised CNC lists for auditory tests. J Speech Hear Disord 1962, 27:62-70.
6. Rance G. Auditory neuropathy/dys-synchrony and it's perceptual consequences. Trends Amplif 2005, 9(1):1-43.
7. Rance G., Corben L., Barker E., et al. Auditory perception in individuals with Friedreich ataxia. Audiol Neurootol 2010, 15:229-240.
8. Rance G., Fava R., Baldock H., et al. Speech perception ability in individuals with Friedeich ataxia. Brain 2008, 131:2002-2012.
9. Rance G., McKay C., Grayden D. Perceptual characterisation of children with auditory neuropathy. Ear Hear 2004, 25:34-46.
10. Spoendlin H. Optic and cochleovestibular degenerations in hereditary ataxias. II. Temporal bone pathology in two cases of Friedreich's ataxia with vestibule-cochlear disorders. Brain 1974, 97:41-48.
11. Subramony S.H., May W., Lynch D., et al. Measuring Friedreich ataxia: interrater reliability of a neurologic rating scale. Neurology 2005, 64:1261-1262.
12. Zeng F.G., Kong Y.Y., Michaelewski H.J., Starr A. Perceptual consequences of disrupted auditory nerve activity. J Neurophysiol 2005, 93:3050-3063.