A murine model of neurofibromatosis type 1 tibial pseudarthrosis featuring proliferative fibrous tissue and osteoclast-like cells

Journal of Bone and Mineral Research

Volumn 27, Issue 1, 2012, Pages 68-78

  El Hoss, Jad ^a,b   Sullivan, Kate ^a,b   Cheng, Tegan ^a   Yu, Nicole Y C ^a   Bobyn, Justin D ^b   Peacock, Lauren ^a   Mikulec, Kathy ^a   Baldock, Paul ^c   Alexander, Ian E ^b   Schindeler, Aaron ^a,b   Little, David G ^a,b  

^a CHILDREN S HOSPITAL AT WESTMEAD   (Australia)

^b UNIVERSITY OF SYDNEY   (Australia)

^c GARVAN INSTITUTE OF MEDICAL RESEARCH   (Australia)

Author keywords

ADENOVIRUS; FRACTURE MODELS; LOCAL GENE KNOCKOUT; NEUROFIBROMATOSIS TYPE 1; ORTHOPEDICS; PSEUDARTHROSIS

Indexed keywords

ACID PHOSPHATASE TARTRATE RESISTANT ISOENZYME; BROXURIDINE; NEUROFIBROMIN; RECOMBINANT BONE MORPHOGENETIC PROTEIN 2;

ADENOVIRUS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CALLUS; CALVARIA; CELL PROLIFERATION; CONGENITAL PSEUDARTHROSIS; CONTROLLED STUDY; FEMALE; FRACTURE NONUNION; GENE INACTIVATION; IN VITRO STUDY; IN VIVO STUDY; MOUSE; NEWBORN; NONHUMAN; OPEN FRACTURE; OSTEOBLAST; OSTEOCLAST; TIBIA CONGENITAL PSEUDARTHROSIS; TIBIA FRACTURE;

ACID PHOSPHATASE; ANIMALS; BONE MORPHOGENETIC PROTEIN 2; CELL DIFFERENTIATION; CELL LINEAGE; CELL PROLIFERATION; DISEASE MODELS, ANIMAL; FEMALE; FIBROSIS; FRACTURE HEALING; GENE DELETION; HEK293 CELLS; HUMANS; INTEGRASES; ISOENZYMES; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MUSCLES; NEUROFIBROMATOSIS 1; NEUROFIBROMIN 1; OSTEOBLASTS; OSTEOCLASTS; OSTEOGENESIS; PSEUDARTHROSIS; RECOMBINANT PROTEINS; REPRODUCIBILITY OF RESULTS; TIBIA; TRANSFORMING GROWTH FACTOR BETA;

EID: 84555189294     PISSN: 08840431     EISSN: 15234681     Source Type: Journal    
DOI: 10.1002/jbmr.528     Document Type: Article

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