Mechanisms regulating superoxide generation in experimental models of phenylketonuria: An essential role of NADPH oxidase

Molecular Genetics and Metabolism

Volumn 104, Issue 3, 2011, Pages 241-248

  Lu, Lihua ^a   Gu, Xuefan ^a   Li, Duan ^a   Liang, Lili ^a   Zhao, Zhen ^b   Gao, Jialin ^a  

^a XINHUA HOSPITAL AFFILIATED TO SHANGHAI JIAO TONG UNIVERSITY SCHOOL OF MEDICINE   (China)

^b SHANGHAI JIAO TONG UNIVERSITY SCHOOL OF MEDICINE   (China)

Author keywords

Cerebral cortex; Cortical neuron; NADPH oxidase; Phenylalanine; Phenylketonuria; Superoxide

Indexed keywords

PHENYLALANINE; PROTEIN P47; PROTEIN P67; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE PHOSPHATE OXIDASE; SUPEROXIDE;

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; BRAIN CORTEX; COLORIMETRY; CONTROLLED STUDY; ENZYME ACTIVITY; IMMUNOFLUORESCENCE; IN VITRO STUDY; MOUSE; NONHUMAN; PHENYLKETONURIA; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN PHOSPHORYLATION; REAL TIME POLYMERASE CHAIN REACTION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; WESTERN BLOTTING; WILD TYPE;

ACETOPHENONES; ANIMALS; BLOTTING, WESTERN; CELLS, CULTURED; CEREBRAL CORTEX; CHROMATOGRAPHY, LIQUID; COLORIMETRY; ETHIDIUM; FLUORESCENT ANTIBODY TECHNIQUE; MICE; MICE, MUTANT STRAINS; NADPH OXIDASE; ONIUM COMPOUNDS; OXIDATIVE STRESS; PHENYLALANINE; PHENYLKETONURIAS; REAL-TIME POLYMERASE CHAIN REACTION; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; SUPEROXIDES; TANDEM MASS SPECTROMETRY;

MUS;

EID: 82455162507     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2011.05.012     Document Type: Article

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