Distribution, clinical features and treatment in Taiwanese patients with symptomatic primary immunodeficiency diseases (PIDs) in a nationwide population-based study during 1985-2010

Immunobiology

Volumn 216, Issue 12, 2011, Pages 1286-1294

  Lee, Wen I ^a,b   Huang, Jing Long ^a,b,k   Jaing, Tang Her ^a,b   Shyur, Shyh Dar ^c   Yang, Kunder D ^b   Chien, Yin Hsiu ^d   Chiang, Bor Luen ^d   Soong, Wen Jue ^e   Chiou, Shyh Shin ^f   Shieh, Chi Chang ^g   Lin, Syh Jae ^b   Yeh, Kuo Wei ^b   Chen, Li Chen ^b   Ou, Liang Shiou ^b   Yao, Tsung Chieh ^b   Lin, Tzou Yien ^b   Chiu, Cheng Hsun ^b   Huang, Yhu Chering ^b   Wu, Kang Hsi ^h   Lin, Ching Yuang ^h   Yu, Hsin Hui ^d   Yang, Yao Hsu ^d   Yu, Hong Ren ^b   Yen, Hsiu Ju ^e   Hsieh, Meng Ying ^b,i   Kuo, Ming Ling ⁱ   Hwu, Wuh Liang ^d   Tsai, Yi Chan ^b   Kuo, Ho Chang ^b   Lin, Yi Ling ^a   Shih, Ying Fan ^a   Chang, Kuei Wen ^j   more..

^a CHANG GUNG UNIVERSITY COLLEGE OF MEDICINE   (Taiwan)

^b CHANG GUNG MEMORIAL HOSPITAL   (Taiwan)

^c MACKAY MEMORIAL HOSPITAL   (Taiwan)

^d NATIONAL TAIWAN UNIVERSITY HOSPITAL   (Taiwan)

^e TAIPEI VETERANS GENERAL HOSPITAL   (Taiwan)

^f KAOHSIUNG MEDICAL UNIVERSITY HOSPITAL   (Taiwan)

^g NATIONAL CHENG KUNG UNIVERSITY HOSPITAL   (Taiwan)

^h CHINA MEDICAL UNIVERSITY HOSPITAL   (Taiwan)

ⁱ CHANG GUNG UNIVERSITY   (Taiwan)

^j Department of Pediatric Gastroenterology   (Taiwan)

^k Chinese Society of Immunology   (Taiwan)

more..

Author keywords

Antibody deficiencies; Chinese; Complement deficiencies; Immunodeficiency; Molecular analysis; Phagocyte defects; Recurrent infections; Taiwan

Indexed keywords

ANTIBIOTIC AGENT; GAMMA INTERFERON; GRANULOCYTE COLONY STIMULATING FACTOR; IMMUNOGLOBULIN;

ADOLESCENT; ADULT; ALBINISM; ARTICLE; AUTOINFLAMMATORY DISEASE; B CELL IMMUNODEFECIENCY; BRONCHIECTASIS; CHEDIAK HIGASHI SYNDROME; CHILD; CHRONIC GRANULOMATOUS DISEASE; CLINICAL FEATURE; COHORT ANALYSIS; COMPLEMENT DEFICIENCY; CONTROLLED STUDY; DISEASE CLASSIFICATION; ERYTHROPHAGOCYTOSIS; FAMILIAL DISEASE; FEMALE; GEOGRAPHIC DISTRIBUTION; HUMAN; HUMORAL IMMUNE DEFICIENCY; IMMUNE DEFICIENCY; IMMUNOGLOBULIN DEFICIENCY; INNATE IMMUNITY; IPEX SYNDROME; LUNG INFECTION; MAJOR CLINICAL STUDY; MALE; NEUTROPENIA; ONSET AGE; PHAGOCYTE DYSFUNCTION; POPULATION RESEARCH; PRIMARY IMMUNODEFICIENCY DISEASE; PRIORITY JOURNAL; PSEUDOMONAS PNEUMONIA; RECURRENT INFECTION; SALMONELLOSIS; SEPTICEMIA; STEM CELL TRANSPLANTATION; STREPTOCOCCUS PNEUMONIA; T CELL IMMUNODEFICIENCY; TAIWAN;

AGE OF ONSET; DNA MUTATIONAL ANALYSIS; FEMALE; HUMANS; IMMUNITY; IMMUNOGLOBULINS, INTRAVENOUS; IMMUNOLOGIC DEFICIENCY SYNDROMES; INCIDENCE; MALE; PREVALENCE; PSEUDOMONAS; RECURRENCE; SEPSIS; STEM CELL TRANSPLANTATION; STREPTOCOCCUS PNEUMONIAE; SURVIVAL ANALYSIS; TAIWAN; TREATMENT OUTCOME;

EID: 80054936417     PISSN: 01712985     EISSN: 18783279     Source Type: Journal    
DOI: 10.1016/j.imbio.2011.06.002     Document Type: Article

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