Misexpression of the Constitutive Rpgr ex1-19 Variant Leads to Severe Photoreceptor Degeneration

Investigative Ophthalmology and Visual Science

Volumn 52, Issue 8, 2011, Pages 5189-5201

  Wright, Rachel N ^a   Hong, Dong Hyun ^a   Perkins, Brian ^b  

^a TEXAS A AND M UNIVERSITY   (United States)

^b TEXAS A AND M UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CONE OPSIN; REGULATOR PROTEIN; RETINITIS PIGMENTOSA GTPASE REGULATOR PROTEIN; UNCLASSIFIED DRUG; CARRIER PROTEIN; EYE PROTEIN; ISOPROTEIN; RPGR PROTEIN, MOUSE;

ALTERNATIVE RNA SPLICING; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ELECTRON MICROSCOPY; GENE; GENE EXPRESSION; GENE MUTATION; HISTOLOGY; IMMUNOBLOTTING; IMMUNOFLUORESCENCE; IMMUNOHISTOCHEMISTRY; MOUSE; NONHUMAN; PHOTORECEPTOR; PRIORITY JOURNAL; PROTEIN ANALYSIS; RETINA DEGENERATION; RETINITIS PIGMENTOSA; RETINITIS PIGMENTOSA GTPASE REGULATOR GENE; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; ANIMAL; C57BL MOUSE; CELL FRACTIONATION; COMPARATIVE STUDY; GENETIC VARIABILITY; GENETICS; GROWTH, DEVELOPMENT AND AGING; HOSPITALIZATION; METABOLISM; NEWBORN; PATHOLOGY; PHOTORECEPTOR CELL; RETINA; TISSUE DISTRIBUTION; TRANSGENIC MOUSE;

ALTERNATIVE SPLICING; ANIMALS; ANIMALS, NEWBORN; CARRIER PROTEINS; EYE PROTEINS; GENE EXPRESSION; GENETIC VARIATION; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; PHOTORECEPTOR CELLS, VERTEBRATE; PROTEIN ISOFORMS; RETINA; RETINAL DEGENERATION; SEVERITY OF ILLNESS INDEX; SUBCELLULAR FRACTIONS; TISSUE DISTRIBUTION;

EID: 80052613455     PISSN: 01460404     EISSN: 15525783     Source Type: Journal    
DOI: 10.1167/iovs.11-7470     Document Type: Article

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