Retinitis Pigmentosa GTPase Regulator (RPGR)-interacting Protein Is Stably Associated with the Photoreceptor Ciliary Axoneme and Anchors RPGR to the Connecting Cilium

Journal of Biological Chemistry

Volumn 276, Issue 15, 2001, Pages 12091-12099

  Hong, Dong Hyun ^b   Yue, Guohua ^b   Adamian, Michael ^b   Li, Tiansen ^a  

^a MASSACHUSETTS EYE AND EAR INFIRMARY   (United States)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

DISEASES; GENES; MUTAGENESIS; PROTEINS;

PHOTORECEPTORS; RETINAL DISEASE;

BIOCHEMISTRY;

GUANINE NUCLEOTIDE BINDING PROTEIN; GUANINE NUCLEOTIDE EXCHANGE FACTOR; OPSIN; PROTEIN; RETINITIS PIGMENTOSA GUANOSINE TRIPHOSPHATASE REGULATOR INTERACTING PROTEIN; UNCLASSIFIED DRUG; CARRIER PROTEIN; COMPLEMENTARY DNA; EYE PROTEIN; RPGR PROTEIN, HUMAN;

AMINO TERMINAL SEQUENCE; ANIMAL TISSUE; ARTICLE; AXONEME; CARBOXY TERMINAL SEQUENCE; CELL DEGENERATION; CELL POLARITY; CONTROLLED STUDY; EXTRACTION; GENE; GENE FUNCTION; GENE MUTATION; IN VIVO STUDY; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; PHENOTYPE; PHOTORECEPTOR; PHOTORECEPTOR CELL; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN LOCALIZATION; PROTEIN PROTEIN INTERACTION; PROTEIN STABILITY; PROTEIN STRUCTURE; RETINA CONE; RETINA ROD; RETINITIS PIGMENTOSA; RETINITIS PIGMENTOSA GUANOSINE TRIPHOSPHATASE REGULATOR GENE; SOLUBILITY; AMINO ACID SEQUENCE; ANIMAL; CELL STRAIN COS1; CHEMISTRY; CILIARY BODY; ELECTRON MICROSCOPY; GENETICS; METABOLISM; MOLECULAR CLONING; MOLECULAR GENETICS; ULTRASTRUCTURE;

ANIMALIA;

AMINO ACID SEQUENCE; ANIMALS; CARRIER PROTEINS; CILIARY BODY; CLONING, MOLECULAR; COS CELLS; DNA, COMPLEMENTARY; EYE PROTEINS; MICE; MICROSCOPY, ELECTRON; MOLECULAR SEQUENCE DATA; PHOTORECEPTORS, VERTEBRATE; PROTEIN BINDING; RETINITIS PIGMENTOSA;

EID: 0035853834     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M009351200     Document Type: Article

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