Coenzyme Q deficiency in muscle

Current Opinion in Neurology

Volumn 24, Issue 5, 2011, Pages 449-456

  Trevisson, Eva ^a   Dimauro, Salvatore ^b   Navas, Placido ^c   Salviati, Leonardo ^a  

^a UNIVERSITY OF PADOVA   (Italy)

^b NewYork Presbyterian Hospital   (United States)

^c UNIVERSIDAD PABLO DE OLAVIDE   (Spain)

Author keywords

CoQ10; CoQ10 deficiency; myopathy; oral supplementation

Indexed keywords

ELECTRON TRANSFERRING FLAVOPROTEIN; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE INHIBITOR; MITOCHONDRIAL DNA; UBIDECARENONE; UBIQUINONE;

ANTIOXIDANT ACTIVITY; BIOENERGY; COENZYME Q DEFICIENCY; DRUG MEGADOSE; ENZYME DEFICIENCY; ENZYME METABOLISM; ENZYME SYNTHESIS; GENE MUTATION; GENETIC DISORDER; HUMAN; HYPERCHOLESTEROLEMIA; MYOPATHY; NONHUMAN; PATHOGENESIS; PHENOTYPE; PYRIMIDINE METABOLISM; REVIEW; SKELETAL MUSCLE;

HUMANS; METABOLIC DISEASES; MITOCHONDRIAL MYOPATHIES; MUSCLE, SKELETAL; MUSCULAR DISEASES; UBIQUINONE;

EID: 80052473671     PISSN: 13507540     EISSN: 14736551     Source Type: Journal    
DOI: 10.1097/WCO.0b013e32834ab528     Document Type: Review

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