Coenzyme Q10 supplementation rescues renal disease in Pdss2 kd/kd mice with mutations in prenyl diphosphate synthase subunit 2

American Journal of Physiology - Renal Physiology

Volumn 295, Issue 5, 2008, Pages

  Saiki, Ryoichi ^a   Lunceford, Adam L ^a   Shi, Yuchen ^a   Marbois, Beth ^a   King, Rhonda ^b   Pachuski, Justin ^b   Kawamukai, Makoto ^c   Gasser, David L ^b   Clarke, Catherine F ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c SHIMANE UNIVERSITY   (Japan)

Author keywords

Antioxidant; Focal segmental glomerulosclerosis; Genetic renal disease; Mitochondrial lipid metabolism; Ubiquinone

Indexed keywords

ALBUMIN; LIPID; LIQSORB; PRENYLDIPHOSPHATE SYNTHASE 1; PRENYLDIPHOSPHATE SYNTHASE 2; SYNTHETASE; UBIDECARENONE; UNCLASSIFIED DRUG; DECAPRENYL PYROPHOSPHATE SYNTHETASE; DRUG DERIVATIVE; PROTEIN SUBUNIT; TRANSFERASE; UBIQUINONE; UBIQUINONE 9;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DIET SUPPLEMENTATION; DISEASE ASSOCIATION; DOSE RESPONSE; DRUG EFFICACY; DRUG MECHANISM; DRUG POTENCY; DRUG TISSUE LEVEL; ESCHERICHIA COLI; FEMALE; FOCAL GLOMERULOSCLEROSIS; GENE MUTATION; GROUPS BY AGE; INTERSTITIAL NEPHRITIS; KIDNEY DISEASE; MALE; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN URINE LEVEL; PROTEINURIA; ALBUMINURIA; ANIMAL; GENE EXPRESSION; GENETIC TRANSFECTION; GENETICS; KIDNEY; LIVER; METABOLISM; MITOCHONDRION; MOUSE MUTANT; MOUSE STRAIN; MUTATION; NEPHRITIS; PATHOLOGY; PROTEIN BINDING; TRANSGENIC MOUSE; URINE;

ALBUMINURIA; ALKYL AND ARYL TRANSFERASES; ANIMALS; DIETARY SUPPLEMENTS; FEMALE; GENE EXPRESSION; GLOMERULOSCLEROSIS, FOCAL SEGMENTAL; KIDNEY; LIVER; MALE; MICE; MICE, INBRED STRAINS; MICE, MUTANT STRAINS; MICE, TRANSGENIC; MITOCHONDRIA; MUTATION; NEPHRITIS; PROTEIN BINDING; PROTEIN SUBUNITS; TRANSFECTION; UBIQUINONE;

EID: 57349192861     PISSN: 1931857X     EISSN: 15221466     Source Type: Journal    
DOI: 10.1152/ajprenal.90445.2008     Document Type: Article

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