Clear cells in the atrioventricular valves of infants with severe human mucopolysaccharidosis (Hurler syndrome) are activated valvular interstitial cells

Cardiovascular Pathology

Volumn 20, Issue 5, 2011, Pages 315-321

  Braunlin, Elizabeth ^a   Tolar, Jakub ^a   MacKey Bojack, Shannon ^b   Masinde, Tiwanda ^c   Krivit, William ^a   Schoen, Frederick J ^d  

^a UNIV OF MINNESOTA HOSP AND CLINIC   (United States)

^b Jesse E Edwards Registry of Cardiovascular Disease   (United States)

^c NATIONAL INSTITUTE OF ENVIRONMENTAL HEALTH SCIENCES   (United States)

^d BRIGHAM AND WOMEN S HOSPITAL   (United States)

Author keywords

Fibroblast; Mucopolysaccharide; Valve

Indexed keywords

CELL MARKER; GELATINASE B; SMOOTH MUSCLE ACTIN; VIMENTIN;

ARTICLE; CASE REPORT; CD34 SELECTION; CELL; CELL ACTIVATION; CHILD; CONTROLLED STUDY; ENDOTHELIAL PROGENITOR CELL; GLYCOSAMINOGLYCAN LADEN CELL; HEART ATRIOVENTRICULAR VALVE; HEMATOPOIETIC STEM CELL; HISTOPATHOLOGY; HUMAN; HUMAN CELL; HUMAN TISSUE; HURLER SYNDROME; IMMUNOHISTOCHEMISTRY; INFANT; MALE; MYOFIBROBLAST; PHENOTYPE; PRIORITY JOURNAL; RETROSPECTIVE STUDY; TISSUE SECTION; VALVULOPLASTY;

BIOLOGICAL MARKERS; FATAL OUTCOME; FIBROBLASTS; GLYCOSAMINOGLYCANS; HUMANS; INFANT; MALE; MITRAL VALVE; MUCOPOLYSACCHARIDOSIS I; TRICUSPID VALVE;

EID: 80052455387     PISSN: 10548807     EISSN: 18791336     Source Type: Journal    
DOI: 10.1016/j.carpath.2010.06.004     Document Type: Article

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