Adjusting diet with sapropterin in phenylketonuria: What factors should be considered?

British Journal of Nutrition

Volumn 106, Issue 2, 2011, Pages 175-182

  MacDonald, Anita ^a   Ahring, Kirsten ^b   Dokoupil, Katharina ^c   Gokmen Ozel, Hulya ^d   Lammardo, Anna Maria ^e   Motzfeldt, Kristina ^f   Robert, Martine ^g   Rocha, Júlio César ^h   Van Rijn, Margreet ⁱ   Bélanger Quintana, Amaya ^j  

^a BIRMINGHAM CHILDREN S HOSPITAL   (United Kingdom)

^b Kennedy Centre   (Denmark)

^c LUDWIG MAXIMILIANS UNIVERSITY   (Germany)

^d HACETTEPE UNIVERSITY   (Turkey)

^e UNIVERSITY OF MILAN   (Italy)

^f OSLO UNIVERSITY HOSPITAL   (Norway)

^g HOP UNIV DES ENFANTS REINE FABIOLA   (Belgium)

^h NATIONAL INSTITUTE OF HEALTH   (Portugal)

ⁱ UNIVERSITY OF GRONINGEN   (Netherlands)

^j HOSPITAL RAMÓN Y CAJAL   (Spain)

more..

Author keywords

Inherited metabolic disorders; Nutrition; Phenylalanine; Phenylketonuria; Sapropterin

Indexed keywords

PHENYLALANINE; SAPROPTERIN; TETRAHYDROBIOPTERIN;

AMINO ACID BLOOD LEVEL; DIET RESTRICTION; DIET THERAPY; DRUG RESPONSE; FOOD QUALITY; HUMAN; INTERVIEW; LONG TERM CARE; PATIENT COMPLIANCE; PATIENT EDUCATION; PATIENT MONITORING; PHENYLKETONURIA; PROTEIN RESTRICTION; RECOMMENDED DRUG DOSE; REVIEW; TREATMENT OUTCOME;

BIOPTERIN; CLINICAL PROTOCOLS; FOOD HABITS; HUMANS; PHENYLALANINE; PHENYLKETONURIAS;

EID: 79960133302     PISSN: 00071145     EISSN: 14752662     Source Type: Journal    
DOI: 10.1017/S0007114511000298     Document Type: Review

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