Large neutral amino acids in the treatment of PKU: From theory to practice

Journal of Inherited Metabolic Disease

Volumn 33, Issue 6, 2010, Pages 671-676

  Van Spronsen, Francjan J ^a   De Groot, Martijn J ^a   Hoeksma, Marieke ^a   Reijngoud, Dirk Jan ^b   Van Rijn, Margreet ^a  

^a UNIVERSITY OF GRONINGEN   (Netherlands)

^b UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; LARGE NEUTRAL AMINO ACID; METHYLPREDNISOLONE ACEPONATE; PHENYLALANINE; TRYPTOPHAN; TYROSINE; UNCLASSIFIED DRUG;

AMINO ACID BRAIN LEVEL; BLOOD BRAIN BARRIER; CLINICAL PRACTICE; COGNITIVE DEFECT; COMPARATIVE EFFECTIVENESS; DIET RESTRICTION; DIET SUPPLEMENTATION; DIETARY INTAKE; DRUG ABSORPTION; DRUG EFFECT; DRUG MECHANISM; HUMAN; NEUROTRANSMITTER UPTAKE; NONHUMAN; OUTCOME ASSESSMENT; PATHOGENESIS; PHENYLKETONURIA; QUALITY OF LIFE; REVIEW; THEORY-PRACTICE RELATIONSHIP; TREATMENT DURATION; TREATMENT OUTCOME; ANIMAL; DEFENSE MECHANISM; DIET THERAPY; ELEMENTAL DIET; EVALUATION; PROFESSIONAL PRACTICE; THEORETICAL MODEL;

AMINO ACIDS, NEUTRAL; ANIMALS; DIETARY SUPPLEMENTS; FOOD, FORMULATED; HUMANS; MODELS, THEORETICAL; PHENYLKETONURIAS; PROFESSIONAL PRACTICE; RATIONALIZATION;

EID: 79952551959     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-010-9216-1     Document Type: Review

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