A metabolomic comparison of mouse models of the Neuronal Ceroid Lipofuscinoses

Journal of Biomolecular NMR

Volumn 49, Issue 3-4, 2011, Pages 175-184

  Salek, Reza M ^a   Pears, Michael R ^a   Cooper, Jonathan D ^b   Mitchison, Hannah M ^c   Pearce, David A ^d   Mortishire Smith, Russell J ^e   Griffin, Julian L ^a,f  

^a UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^b KING'S COLLEGE LONDON   (United Kingdom)

^c ROYAL FREE AND UNIVERSITY COLLEGE MEDICAL SCHOOL   (United Kingdom)

^d UNIVERSITY OF SOUTH DAKOTA   (United States)

^e JOHNSON AND JOHNSON   (United States)

^f UNIVERSITY OF CAMBRIDGE   (United Kingdom)

Author keywords

Batten disease; CLN3; Juvenile Neuronal Ceroid Lipofuscinosis (JNCL); Metabolomics; Neurodegeneration; NMR

Indexed keywords

4 AMINOBUTYRIC ACID; BRAIN EXTRACT; GLUTAMIC ACID; GLUTAMINE;

AMINO ACID METABOLISM; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN CORTEX; CEREBELLUM; COMPARATIVE STUDY; CONTROLLED STUDY; DISEASE CLASSIFICATION; METABOLOMICS; MOTONEURON; MOUSE; NERVE DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL;

ANIMALS; CEREBELLUM; CEREBRAL CORTEX; DISEASE MODELS, ANIMAL; GLUTAMIC ACID; GLUTAMINE; MAGNETIC RESONANCE SPECTROSCOPY; MICE; NEURONAL CEROID-LIPOFUSCINOSES; NEURONS; PIGMENTS, BIOLOGICAL;

ANIMALIA; MUS;

EID: 79958769605     PISSN: 09252738     EISSN: 15735001     Source Type: Journal    
DOI: 10.1007/s10858-011-9491-7     Document Type: Article

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