Aspartoacylase deficiency affects early postnatal development of oligodendrocytes and myelination

Neurobiology of Disease

Volumn 40, Issue 2, 2010, Pages 432-443

  Mattan, Natalia S ^a   Ghiani, Cristina A ^a   Lloyd, Marcia ^a,b   Matalon, Reuben ^c   Bok, Dean ^a,b   Casaccia, Patrizia ^d   de Vellis, Jean ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b JULES STEIN EYE INSTITUTE   (United States)

^c University of Texas Medical Branch School of Medicine   (United States)

^d MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

Aspartoacylase; Canavan disease; Development; Leukodystrophy; Neural cells; Oligodendrocytes

Indexed keywords

2',3' CYCLIC NUCLEOTIDE 3' PHOSPHODIESTERASE; ASPARTOACYLASE; CERAMIDE GALACTOSYLTRANSFERASE; GALACTOSYLTRANSFERASE; GLIAL FIBRILLARY ACIDIC PROTEIN; GLYCERALDEHYDE 3 PHOSPHATE DEHYDROGENASE; HISTONE H3; MYELIN ASSOCIATED GLYCOPROTEIN; MYELIN PROTEIN; NUCLEAR FACTOR I; PHOSPHOLIPASE; PLATELET DERIVED GROWTH FACTOR ALPHA RECEPTOR; UNCLASSIFIED DRUG;

ACETYLATION; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTOSIS; BRAIN DEVELOPMENT; CANAVAN DISEASE; CELL MATURATION; CELLULAR DISTRIBUTION; CHROMATIN; CONTROLLED STUDY; DEGENERATIVE DISEASE; ENZYME DEFICIENCY; MOUSE; MYELINATION; NONHUMAN; OLIGODENDROGLIA; POSTNATAL DEVELOPMENT; PRIORITY JOURNAL; PROTEIN EXPRESSION; WILD TYPE;

AMIDOHYDROLASES; ANIMALS; BIOLOGICAL MARKERS; BLOTTING, WESTERN; BRAIN; CANAVAN DISEASE; CHROMATIN; DISEASE MODELS, ANIMAL; GLIAL FIBRILLARY ACIDIC PROTEIN; HISTONES; IMMUNOHISTOCHEMISTRY; MICE; MICE, KNOCKOUT; MICROSCOPY, ELECTRON; MYELIN SHEATH; OLIGODENDROGLIA; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; TIME FACTORS;

EID: 79958003786     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2010.07.003     Document Type: Article

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