Lack of activation of the unfolded protein response in mouse and cellular models of Niemann-Pick type C disease

Neurodegenerative Diseases

Volumn 8, Issue 3, 2011, Pages 124-128

  Klein, Andres ^a   Mosqueira, Matías ^a   Martínez, Gabriela ^c   Robledo, Fermín ^a   González, Marcela ^a   Caballero, Benjamín ^c   Cancino, Gonzalo I ^b   Alvarez, Alejandra R ^b   Hetz, Claudio ^c,d   Zanlungo, Silvana ^a  

^a Facultad de Medicina   (Chile)

^b PONTIFICIA UNIVERSIDAD CATÓLICA DE CHILE   (Chile)

^c UNIVERSITY OF CHILE   (Chile)

^d HARVARD SCHOOL OF PUBLIC HEALTH   (United States)

Author keywords

Apoptosis; Cholesterol; Endoplasmic reticulum stress; Niemann Pick type C; Unfolded protein response

Indexed keywords

CHOLESTEROL;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CEREBELLUM; CONTROLLED STUDY; ENDOPLASMIC RETICULUM STRESS; GENE EXPRESSION; GENE SILENCING; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; REAL TIME POLYMERASE CHAIN REACTION; UNFOLDED PROTEIN RESPONSE;

ANIMALS; APOPTOSIS; CEREBELLUM; CHOLESTEROL; DISEASE MODELS, ANIMAL; ENDOPLASMIC RETICULUM; MICE; MICE, KNOCKOUT; NEURONS; NIEMANN-PICK DISEASE, TYPE C; PROTEINS; SIGNAL TRANSDUCTION; UNFOLDED PROTEIN RESPONSE;

EID: 79953316609     PISSN: 16602854     EISSN: 16602862     Source Type: Journal    
DOI: 10.1159/000316540     Document Type: Article

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