-
1
-
-
0033695135
-
Muscle size and cardiorespiratory response to exercise in cystic fibrosis
-
Moser C, Tirakitsoontorn P, Nussbaum E, Newcomb R, Cooper DM 2000 Muscle size and cardiorespiratory response to exercise in cystic fibrosis. Am J Respir Crit Care Med 162:1823-1827
-
(2000)
Am J Respir Crit Care Med
, vol.162
, pp. 1823-1827
-
-
Moser, C.1
Tirakitsoontorn, P.2
Nussbaum, E.3
Newcomb, R.4
Cooper, D.M.5
-
2
-
-
0345732432
-
Longitudinal determinants of peak aerobic performance in children with cystic fibrosis
-
Klijn PH, Van Der Net J, Kimpen JL, Helders PJ, Van Der Ent CK 2003 Longitudinal determinants of peak aerobic performance in children with cystic fibrosis. Chest 124:2215-2219
-
(2003)
Chest
, vol.124
, pp. 2215-2219
-
-
Klijn, P.H.1
Van Der Net, J.2
Kimpen, J.L.3
Helders, P.J.4
Van Der Ent, C.K.5
-
3
-
-
0032942306
-
Effects of hyperoxia on oxygen uptake kinetics in cystic fibrosis patients as determined by pseudo
-
random binary sequence exercise
-
Kusenbach G, Wieching R, Barker M, Hoffmann U, Essfeld D 1999 Effects of hyperoxia on oxygen uptake kinetics in cystic fibrosis patients as determined by pseudo-random binary sequence exercise. Eur J Appl Physiol Occup Physiol 79:192-196
-
(1999)
Eur J Appl Physiol Occup Physiol
, vol.79
, pp. 192-196
-
-
Kusenbach, G.1
Wieching, R.2
Barker, M.3
Hoffmann, U.4
Essfeld, D.5
-
4
-
-
66749087511
-
Non-invasive assessment of exercise performance in children with cystic fibrosis (CF) and non-cystic fibrosis bronchiectasis: Is there a CF specific muscle defect?
-
Rosenthal M, Narang I, Edwards L, Bush A 2009 Non-invasive assessment of exercise performance in children with cystic fibrosis (CF) and non-cystic fibrosis bronchiectasis: is there a CF specific muscle defect? Pediatr Pulmonol 44:222-230
-
(2009)
Pediatr Pulmonol
, vol.44
, pp. 222-230
-
-
Rosenthal, M.1
Narang, I.2
Edwards, L.3
Bush, A.4
-
5
-
-
0026755299
-
Cloning and sequence analysis of rat cystic fibrosis transmembrane conductance regulator
-
Fiedler MA, Nemecz ZK, Shull GE 1992 Cloning and sequence analysis of rat cystic fibrosis transmembrane conductance regulator. Am J Physiol 262:L779-L784
-
(1992)
Am J Physiol
, vol.262
-
-
Fiedler, M.A.1
Nemecz, Z.K.2
Shull, G.E.3
-
6
-
-
68249094323
-
Lack of CFTR in skeletal muscle predisposes to muscle wasting and diaphragm muscle pump failure in cystic fibrosis mice
-
Divangahi M, Balghi H, Danialou G, Comtois AS, Demoule A, Ernest S, Haston C, Robert R, Hanrahan JW, Radzioch D, Petrof BJ 2009 Lack of CFTR in skeletal muscle predisposes to muscle wasting and diaphragm muscle pump failure in cystic fibrosis mice. PLoS Genet 5:e1000586
-
(2009)
PLoS Genet
, vol.5
-
-
Divangahi, M.1
Balghi, H.2
Danialou, G.3
Comtois, A.S.4
Demoule, A.5
Ernest, S.6
Haston, C.7
Robert, R.8
Hanrahan, J.W.9
Radzioch, D.10
Petrof, B.J.11
-
7
-
-
77952899083
-
Cystic fibrosis transmembrane conductance regulator in human muscle. Dysfunction causes abnormal metabolic recovery in exercise
-
Lamhonwah AM, Bear CE, Huan LJ, Kim Chiaw P, Ackerley CA, Tein I 2010 Cystic fibrosis transmembrane conductance regulator in human muscle. Dysfunction causes abnormal metabolic recovery in exercise. Ann Neurol 67:802-808
-
(2010)
Ann Neurol
, vol.67
, pp. 802-808
-
-
Lamhonwah, A.M.1
Bear, C.E.2
Huan, L.J.3
Kim Chiaw, P.4
Ackerley, C.A.5
Tein, I.6
-
8
-
-
0031968323
-
Determinants of aerobic and anaerobic exercise performance in cystic fibrosis
-
Shah AR, Gozal D, Keens TG 1998 Determinants of aerobic and anaerobic exercise performance in cystic fibrosis. Am J Respir Crit Care Med 157:1145-1150
-
(1998)
Am J Respir Crit Care Med
, vol.157
, pp. 1145-1150
-
-
Shah, A.R.1
Gozal, D.2
Keens, T.G.3
-
9
-
-
0347362534
-
Muscle Function and Resting Energy Expenditure in Female Athletes with Cystic Fibrosis
-
DOI 10.1164/rccm.200303-363OC
-
Selvadurai HC, Allen J, Sachinwalla T, Macauley J, Blimkie CJ, Van Asperen PP 2003 Muscle function and resting energy expenditure in female athletes with cystic fibrosis. Am J Respir Crit Care Med 168:1476-1480 (Pubitemid 38037332)
-
(2003)
American Journal of Respiratory and Critical Care Medicine
, vol.168
, Issue.12
, pp. 1476-1480
-
-
Selvadurai, H.C.1
Allen, J.2
Sachinwalla, T.3
Macauley, J.4
Blimkie, C.J.5
Van Asperen, P.P.6
-
10
-
-
0031795068
-
Inspiratory muscle function and body composition in cystic fibrosis
-
Ionescu AA, Chatham K, Davies CA, Nixon LS, Enright S, Shale DJ 1998 Inspiratory muscle function and body composition in cystic fibrosis. Am J Respir Crit Care Med 158:1271-1276
-
(1998)
Am J Respir Crit Care Med
, vol.158
, pp. 1271-1276
-
-
Ionescu, A.A.1
Chatham, K.2
Davies, C.A.3
Nixon, L.S.4
Enright, S.5
Shale, D.J.6
-
11
-
-
0032986142
-
Peripheral muscle weakness and exercise capacity in children with cystic fibrosis
-
De Meer K, Gulmans VA, Van Der Laag J 1999 Peripheral muscle weakness and exercise capacity in children with cystic fibrosis. Am J Respir Crit Care Med 159:748-754
-
(1999)
Am J Respir Crit Care Med
, vol.159
, pp. 748-754
-
-
De Meer, K.1
Gulmans, V.A.2
Van Der Laag, J.3
-
12
-
-
19844365349
-
Muscular strength and function in patients with cystic fibrosis
-
Sahlberg ME, Svantesson U, Thomas EM, Strandvik B 2005 Muscular strength and function in patients with cystic fibrosis. Chest 127:1587-1592
-
(2005)
Chest
, vol.127
, pp. 1587-1592
-
-
Sahlberg, M.E.1
Svantesson, U.2
Thomas, E.M.3
Strandvik, B.4
-
13
-
-
0034523134
-
Clinical utility of muscle MR spectroscopy
-
Taylor DJ 2000 Clinical utility of muscle MR spectroscopy. Semin Musculoskelet Radiol 4:481-502
-
(2000)
Semin Musculoskelet Radiol
, vol.4
, pp. 481-502
-
-
Taylor, D.J.1
-
14
-
-
0031035820
-
Adenosine triphosphate production rates metabolic economy calculations pH, phosphomonoesters, phosphodiesters, and force output during short-duration maximal isometric plantar flexion exercises and repeated maximal isometric plantar flexion exercises
-
Newcomer BR, Boska MD 1997 Adenosine triphosphate production rates metabolic economy calculations pH, phosphomonoesters, phosphodiesters, and force output during short-duration maximal isometric plantar flexion exercises and repeated maximal isometric plantar flexion exercises. Muscle Nerve 20:336-346
-
(1997)
Muscle Nerve
, vol.20
, pp. 336-346
-
-
Newcomer, B.R.1
Boska, M.D.2
-
15
-
-
1942504916
-
P-31 magnetic resonance spectroscopy. A tool for diagnostic purposes and pathophysiological insights in muscle diseases
-
Mattei JP, Bendahan D, Cozzone P 2004 P-31 magnetic resonance spectroscopy. A tool for diagnostic purposes and pathophysiological insights in muscle diseases. Reumatismo 56:9-14
-
(2004)
Reumatismo
, vol.56
, pp. 9-14
-
-
Mattei, J.P.1
Bendahan, D.2
Cozzone, P.3
-
16
-
-
0442313529
-
Primary ciliary dyskinesia: Diagnostic and phenotypic features
-
Noone PG, Leigh MW, Sannuti A, Minnix SL, Carson JL, Hazucha M, Zariwala MA, Knowles MR 2004 Primary ciliary dyskinesia: diagnostic and phenotypic features. Am J Respir Crit Care Med 169:459-467
-
(2004)
Am J Respir Crit Care Med
, vol.169
, pp. 459-467
-
-
Noone, P.G.1
Leigh, M.W.2
Sannuti, A.3
Minnix, S.L.4
Carson, J.L.5
Hazucha, M.6
Zariwala, M.A.7
Knowles, M.R.8
-
17
-
-
36849090559
-
Primary ciliary dyskinesia: Current state of the art
-
Bush A, Chodhari R, Collins N, Copeland F, Hall P, Harcourt J, Hariri M, Hogg C, Lucas J, Mitchison HM, O'Callaghan C, Phillips G 2007 Primary ciliary dyskinesia: current state of the art. Arch Dis Child 92:1136-1140
-
(2007)
Arch Dis Child
, vol.92
, pp. 1136-1140
-
-
Bush, A.1
Chodhari, R.2
Collins, N.3
Copeland, F.4
Hall, P.5
Harcourt, J.6
Hariri, M.7
Hogg, C.8
Lucas, J.9
Mitchison, H.M.10
O'Callaghan, C.11
Phillips, G.12
-
18
-
-
55049133473
-
Assessment of body composition in pediatric patients with cystic fibrosis
-
Wells GD, Heale L, Schneiderman JE, Wilkes DL, Atenafu E, Coates AL, Ratjen F 2008 Assessment of body composition in pediatric patients with cystic fibrosis. Pediatr Pulmonol 43:1025-1032
-
(2008)
Pediatr Pulmonol
, vol.43
, pp. 1025-1032
-
-
Wells, G.D.1
Heale, L.2
Schneiderman, J.E.3
Wilkes, D.L.4
Atenafu, E.5
Coates, A.L.6
Ratjen, F.7
-
19
-
-
21744460289
-
Standardisation of spirometry
-
Miller MR, Hankinson J, Brusasco V, Burgos F, Casaburi R, Coates A, Crapo R, Enright P, Van Der Grinten CP, Gustafsson P, Jensen R, Johnson DC, MacIntyre N, McKay R, Navajas D, Pedersen OF, Pellegrino R, Viegi G, Wanger J 2005 Standardisation of spirometry. Eur Respir J 26:319-338
-
(2005)
Eur Respir J
, vol.26
, pp. 319-338
-
-
Miller, M.R.1
Hankinson, J.2
Brusasco, V.3
Burgos, F.4
Casaburi, R.5
Coates, A.6
Crapo, R.7
Enright, P.8
Van Der Grinten, C.P.9
Gustafsson, P.10
Jensen, R.11
Johnson, D.C.12
MacIntyre, N.13
McKay, R.14
Navajas, D.15
Pedersen, O.F.16
Pellegrino, R.17
Viegi, G.18
Wanger, J.19
-
20
-
-
0017097945
-
Five- to seven-year course of pulmonary function in cystic fibrosis
-
Corey M, Levison H, Crozier D 1976 Five- to seven-year course of pulmonary function in cystic fibrosis. Am Rev Respir Dis 114:1085-1092
-
(1976)
Am Rev Respir Dis
, vol.114
, pp. 1085-1092
-
-
Corey, M.1
Levison, H.2
Crozier, D.3
-
21
-
-
0015059627
-
Cardio-respiratory response to exercise in normal children
-
Godfrey S, Davies CT, Wozniak E, Barnes CA 1971 Cardio-respiratory response to exercise in normal children. Clin Sci 40:419-431
-
(1971)
Clin Sci
, vol.40
, pp. 419-431
-
-
Godfrey, S.1
Davies, C.T.2
Wozniak, E.3
Barnes, C.A.4
-
22
-
-
33646580393
-
Development of the habitual activity estimation scale for clinical research: A systematic approach
-
Hay JA, Cairney J 2006 Development of the habitual activity estimation scale for clinical research: a systematic approach. Pediatr Exerc Sci 18:193-202
-
(2006)
Pediatr Exerc Sci
, vol.18
, pp. 193-202
-
-
Hay, J.A.1
Cairney, J.2
-
23
-
-
25144489764
-
Sex differences in habitual physical activity and lung function decline in children with cystic fibrosis
-
Schneiderman-Walker J, Wilkes DL, Strug L, Lands LC, Pollock SL, Selvadurai HC, Hay J, Coates AL, Corey M 2005 Sex differences in habitual physical activity and lung function decline in children with cystic fibrosis. J Pediatr 147:321-326
-
(2005)
J Pediatr
, vol.147
, pp. 321-326
-
-
Schneiderman-Walker, J.1
Wilkes, D.L.2
Strug, L.3
Lands, L.C.4
Pollock, S.L.5
Selvadurai, H.C.6
Hay, J.7
Coates, A.L.8
Corey, M.9
-
24
-
-
42149121530
-
Reliability and validity of the habitual activity estimation scale (HAES) in patients with cystic fibrosis
-
Wells GD, Wilkes DL, Schneiderman-Walker J, Elmi M, Tullis E, Lands LC, Ratjen F, Coates AL 2008 Reliability and validity of the habitual activity estimation scale (HAES) in patients with cystic fibrosis. Pediatr Pulmonol 43:345-353
-
(2008)
Pediatr Pulmonol
, vol.43
, pp. 345-353
-
-
Wells, G.D.1
Wilkes, D.L.2
Schneiderman-Walker, J.3
Elmi, M.4
Tullis, E.5
Lands, L.C.6
Ratjen, F.7
Coates, A.L.8
-
25
-
-
0027336018
-
31P-magnetic resonance spectroscopy of leg muscle metabolism during exercise in children and adults
-
Zanconato S, Buchthal S, Barstow TJ, Cooper DM 1993 31P-magnetic resonance spectroscopy of leg muscle metabolism during exercise in children and adults. J Appl Physiol 74:2214-2218
-
(1993)
J Appl Physiol
, vol.74
, pp. 2214-2218
-
-
Zanconato, S.1
Buchthal, S.2
Barstow, T.J.3
Cooper, D.M.4
-
26
-
-
0028341514
-
ATP production rates as a function of force level in the human gastrocnemius/soleus using 31P MRS
-
Boska M 1994 ATP production rates as a function of force level in the human gastrocnemius/soleus using 31P MRS. Magn Reson Med 32:1-10
-
(1994)
Magn Reson Med
, vol.32
, pp. 1-10
-
-
Boska, M.1
-
27
-
-
0021871768
-
Cerebral intracellular pH by 31P nuclear magnetic resonance spectroscopy
-
Petroff OA, Prichard JW, Behar KL, Alger JR, Den Hollander JA, Shulman RG 1985 Cerebral intracellular pH by 31P nuclear magnetic resonance spectroscopy. Neurology 35:781-788
-
(1985)
Neurology
, vol.35
, pp. 781-788
-
-
Petroff, O.A.1
Prichard, J.W.2
Behar, K.L.3
Alger, J.R.4
Den Hollander, J.A.5
Shulman, R.G.6
-
28
-
-
0033623687
-
In vivo (31)P-MRS assessment of cytosolic [Mg(2 + )] in the human skeletal muscle in different metabolic conditions
-
Iotti S, Frassineti C, Alderighi L, Sabatini A, Vacca A, Barbiroli B 2000 In vivo (31)P-MRS assessment of cytosolic [Mg(2 + )] in the human skeletal muscle in different metabolic conditions. Magn Reson Imaging 18:607-614
-
(2000)
Magn Reson Imaging
, vol.18
, pp. 607-614
-
-
Iotti, S.1
Frassineti, C.2
Alderighi, L.3
Sabatini, A.4
Vacca, A.5
Barbiroli, B.6
-
29
-
-
0022610771
-
Anaerobic characteristics in male children and adolescents
-
Inbar O, Bar-Or O 1986 Anaerobic characteristics in male children and adolescents. Med Sci Sports Exerc 18:264-269
-
(1986)
Med Sci Sports Exerc
, vol.18
, pp. 264-269
-
-
Inbar, O.1
Bar-Or, O.2
-
31
-
-
24944480842
-
Revisiting cystic fibrosis transmembrane conductance regulator structure and function
-
Hanrahan JW, Wioland MA 2004 Revisiting cystic fibrosis transmembrane conductance regulator structure and function. Proc Am Thorac Soc 1:17-21
-
(2004)
Proc Am Thorac Soc
, vol.1
, pp. 17-21
-
-
Hanrahan, J.W.1
Wioland, M.A.2
-
34
-
-
0038749611
-
Control of dynamic CFTR selectivity by glutamate and ATP in epithelial cells
-
Reddy MM, Quinton PM 2003 Control of dynamic CFTR selectivity by glutamate and ATP in epithelial cells. Nature 423:756-760
-
(2003)
Nature
, vol.423
, pp. 756-760
-
-
Reddy, M.M.1
Quinton, P.M.2
-
35
-
-
33645779525
-
Non-invasive investigation of muscle function using 31P magnetic resonance spectroscopy and 1H MR imaging
-
Bendahan D, Mattei JP, Guis S, Kozak-Ribbens G, Cozzone PJ 2006 [Non-invasive investigation of muscle function using 31P magnetic resonance spectroscopy and 1H MR imaging]. Rev Neurol (Paris) 162:467-484
-
(2006)
Rev Neurol (Paris)
, vol.162
, pp. 467-484
-
-
Bendahan, D.1
Mattei, J.P.2
Guis, S.3
Kozak-Ribbens, G.4
Cozzone, P.J.5
-
37
-
-
20444461559
-
Symptoms, lactate and exercise limitation at peak cycle ergometry in adults with cystic fibrosis
-
Moorcroft AJ, Dodd ME, Morris J, Webb AK 2005 Symptoms, lactate and exercise limitation at peak cycle ergometry in adults with cystic fibrosis. Eur Respir J 25:1050-1056
-
(2005)
Eur Respir J
, vol.25
, pp. 1050-1056
-
-
Moorcroft, A.J.1
Dodd, M.E.2
Morris, J.3
Webb, A.K.4
-
38
-
-
36849085908
-
Lung disease severity, chronic inflammation, iron deficiency, and erythropoietin response in adults with cystic fibrosis
-
Fischer R, Simmerlein R, Huber RM, Schiffl H, Lang SM 2007 Lung disease severity, chronic inflammation, iron deficiency, and erythropoietin response in adults with cystic fibrosis. Pediatr Pulmonol 42:1193-1197
-
(2007)
Pediatr Pulmonol
, vol.42
, pp. 1193-1197
-
-
Fischer, R.1
Simmerlein, R.2
Huber, R.M.3
Schiffl, H.4
Lang, S.M.5
-
39
-
-
33744498612
-
Markers of airway inflammation in primary ciliary dyskinesia studied using exhaled breath condensate
-
Zihlif N, Paraskakis E, Tripoli C, Lex C, Bush A 2006 Markers of airway inflammation in primary ciliary dyskinesia studied using exhaled breath condensate. Pediatr Pulmonol 41:509-514
-
(2006)
Pediatr Pulmonol
, vol.41
, pp. 509-514
-
-
Zihlif, N.1
Paraskakis, E.2
Tripoli, C.3
Lex, C.4
Bush, A.5
|