Cystic fibrosis transmembrane conductance regulator in human muscle dysfunction causes abnormal metabolic recovery in exercise

Annals of Neurology

Volumn 67, Issue 6, 2010, Pages 802-808

  Lamhonwah, Anne Marie ^a,b   Bear, Christine E ^a   Huan, Ling Jun ^a   Chiaw, Patrick Kim ^a   Ackerley, Cameron A ^a   Tein, Ingrid ^a,b  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

CHLORIDE CHANNEL; FORSKOLIN; RYANODINE RECEPTOR; SARCOPLASMIC RETICULUM CALCIUM TRANSPORTING ADENOSINE TRIPHOSPHATASE; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ARTICLE; CALCIUM HOMEOSTASIS; CONTROLLED STUDY; CYSTIC FIBROSIS; EXCITATION CONTRACTION COUPLING; EXERCISE; HUMAN; HUMAN TISSUE; MUSCLE CELL; MUSCLE METABOLISM; MUSCLE WEAKNESS; PHOSPHORUS NUCLEAR MAGNETIC RESONANCE; PRIORITY JOURNAL; PROTEIN EXPRESSION; SARCOLEMMA; SARCOPLASM; SKELETAL MUSCLE;

ANIMALS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EXERCISE; FEMALE; FORSKOLIN; GENE EXPRESSION REGULATION; HUMANS; MAGNETIC RESONANCE SPECTROSCOPY; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, IMMUNOELECTRON; MUSCLE, SKELETAL; MUTATION; PHOSPHODIESTERASE INHIBITORS; SARCOLEMMA; SUBCELLULAR FRACTIONS;

EID: 77952899083     PISSN: 03645134     EISSN: 15318249     Source Type: Journal    
DOI: 10.1002/ana.21982     Document Type: Article

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