Familial interstitial pulmonary fibrosis: A large family with atypical clinical features;La fibrose pulmonaire interstitielle familiale: Une grande famille aux manifestations cliniques atypiques

Canadian Respiratory Journal

Volumn 17, Issue 6, 2010, Pages 269-274

  Chibbar, Ranji ^a   Gjevre, John A ^b   Shih, Francis ^a   Neufeld, Heather ^a   Lemire, Edmond G ^c   Fladeland, Derek A ^d   Cockcroft, Donald W ^b  

^a Division of Respirology   (Canada)

^b Department of Pediatrics ^*  (Canada)

^c Division of Medical Genetics   (Canada)

^d ROYAL UNIVERSITY HOSPITAL   (Canada)

Author keywords

ABCA3; Familial pulmonary fibrosis; Idiopathic pulmonary fibrosis; Surfactant protein C; Telomerase; Usual interstitial pneumonia

Indexed keywords

ABC TRANSPORTER; ABC TRANSPORTER A3; DNA; SURFACTANT PROTEIN C; TELOMERASE; TELOMERASE REVERSE TRANSCRIPTASE; TELOMERASE TERC; UNCLASSIFIED DRUG;

ADULT; AMINO ACID SUBSTITUTION; ARTICLE; CLINICAL ARTICLE; CLINICAL FEATURE; COMPUTER ASSISTED TOMOGRAPHY; DISEASE COURSE; DNA POLYMORPHISM; FAMILIAL DISEASE; FEMALE; FIBROSING ALVEOLITIS; GENETIC ANALYSIS; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; LUNG BIOPSY; MALE; NUCLEIC ACID BASE SUBSTITUTION; PEDIGREE; PRIORITY JOURNAL; SEQUENCE ALIGNMENT; SINGLE NUCLEOTIDE POLYMORPHISM; THORAX RADIOGRAPHY;

EID: 78650687751     PISSN: 11982241     EISSN: None     Source Type: Journal    
DOI: 10.1155/2010/591523     Document Type: Article

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