-
1
-
-
0001025080
-
Erythropoietic protoporphyria. A new porphyria syndrome with solar urticaria due to protoporphyrinaemia
-
Magnus IA, Jarrett A, Prankerd TA, Rimington C. Erythropoietic protoporphyria. A new porphyria syndrome with solar urticaria due to protoporphyrinaemia. Lancet 1961; 2: 448-451
-
(1961)
Lancet
, vol.2
, pp. 448-451
-
-
Magnus, I.A.1
Jarrett, A.2
Prankerd, T.A.3
Rimington, C.4
-
2
-
-
0027360547
-
Biochemistry of porphyria
-
Moore MR. Biochemistry of porphyria. Int J Biochem 1993; 25: 1353-1368
-
(1993)
Int J Biochem
, vol.25
, pp. 1353-1368
-
-
Moore, M.R.1
-
3
-
-
70350622441
-
The acute porphyrias: A diagnostic and therapeutic challenge in internal and emergency medicine
-
Ventura P, Cappellini MD, Rocchi E. The acute porphyrias: a diagnostic and therapeutic challenge in internal and emergency medicine. Intern Emerg Med 2009; 4: 297-308
-
(2009)
Intern Emerg Med
, vol.4
, pp. 297-308
-
-
Ventura, P.1
Cappellini, M.D.2
Rocchi, E.3
-
4
-
-
0034351813
-
Erythropoietic protoporphyria. An overview with emphasis on the liver
-
Meerman L. Erythropoietic protoporphyria. An overview with emphasis on the liver. Scand J Gastroenterol Suppl 2000; 79-85
-
(2000)
Scand J Gastroenterol Suppl
, pp. 79-85
-
-
Meerman, L.1
-
5
-
-
48249103159
-
Erythropoietic porphyrias: Animal models and update in gene-based therapies
-
Richard E, Robert-Richard E, Ged C, Moreau-Gaudry F, de Verneuil H. Erythropoietic porphyrias: animal models and update in gene-based therapies. Curr Gene Ther 2008; 8: 176-186
-
(2008)
Curr Gene Ther
, vol.8
, pp. 176-186
-
-
Richard, E.1
Robert-Richard, E.2
Ged, C.3
Moreau-Gaudry, F.4
de Verneuil, H.5
-
6
-
-
67651163473
-
Post-transcriptional regulation of the expression of ferrochelatase by its variant mRNA
-
Sakaino M, Kataoka T, Taketani S. Post-transcriptional regulation of the expression of ferrochelatase by its variant mRNA. J Biochem 2009; 145: 733-738
-
(2009)
J Biochem
, vol.145
, pp. 733-738
-
-
Sakaino, M.1
Kataoka, T.2
Taketani, S.3
-
7
-
-
37849001329
-
Identification of a ferrochelatase mutation in a Chinese family with erythropoietic protoporphyria
-
Kong XF, Ye J, Gao DY, Gong QM, Zhang DH, Lu ZM, Lu YM, Zhang XX. Identification of a ferrochelatase mutation in a Chinese family with erythropoietic protoporphyria. J Hepatol 2008; 48: 375-379
-
(2008)
J Hepatol
, vol.48
, pp. 375-379
-
-
Kong, X.F.1
Ye, J.2
Gao, D.Y.3
Gong, Q.M.4
Zhang, D.H.5
Lu, Z.M.6
Lu, Y.M.7
Zhang, X.X.8
-
8
-
-
51149108520
-
C-terminal deletions in the ALAS2 gene lead to gain of function and cause X-linked dominant protoporphyria without anemia or iron overload
-
Whatley SD, Ducamp S, Gouya L, Grandchamp B, Beaumont C, Badminton MN, Elder GH, Holme SA, Anstey AV, Parker M, Corrigall AV, Meissner PN, Hift RJ, Marsden JT, Ma Y, Mieli-Vergani G, Deybach JC, Puy H. C-terminal deletions in the ALAS2 gene lead to gain of function and cause X-linked dominant protoporphyria without anemia or iron overload. Am J Hum Genet 2008; 83: 408-414
-
(2008)
Am J Hum Genet
, vol.83
, pp. 408-414
-
-
Whatley, S.D.1
Ducamp, S.2
Gouya, L.3
Grandchamp, B.4
Beaumont, C.5
Badminton, M.N.6
Elder, G.H.7
Holme, S.A.8
Anstey, A.V.9
Parker, M.10
Corrigall, A.V.11
Meissner, P.N.12
Hift, R.J.13
Marsden, J.T.14
Ma, Y.15
Mieli-Vergani, G.16
Deybach, J.C.17
Puy, H.18
-
9
-
-
37049019507
-
Erythropoiesis and iron metabolism in dominant erythropoietic protoporphyria
-
Holme SA, Worwood M, Anstey AV, Elder GH, Badminton MN. Erythropoiesis and iron metabolism in dominant erythropoietic protoporphyria. Blood 2007; 110: 4108-4110
-
(2007)
Blood
, vol.110
, pp. 4108-4110
-
-
Holme, S.A.1
Worwood, M.2
Anstey, A.V.3
Elder, G.H.4
Badminton, M.N.5
-
10
-
-
35648929413
-
Erythropoietic protoporphyria with eye complications
-
Tsuboi H, Yonemoto K, Katsuoka K. Erythropoietic protoporphyria with eye complications. J Dermatol 2007; 34: 790-794
-
(2007)
J Dermatol
, vol.34
, pp. 790-794
-
-
Tsuboi, H.1
Yonemoto, K.2
Katsuoka, K.3
-
12
-
-
34347241782
-
Liver disease in erythropoietic protoporphyria: Insights and implications for management
-
Anstey AV, Hift RJ. Liver disease in erythropoietic protoporphyria: insights and implications for management. Gut 2007; 56: 1009-1018
-
(2007)
Gut
, vol.56
, pp. 1009-1018
-
-
Anstey, A.V.1
Hift, R.J.2
-
14
-
-
33749234364
-
Modern diagnosis and management of the porphyrias
-
Sassa S. Modern diagnosis and management of the porphyrias. Br J Haematol 2006; 135: 281-292
-
(2006)
Br J Haematol
, vol.135
, pp. 281-292
-
-
Sassa, S.1
-
15
-
-
0034523846
-
Porphyrins, porphyrin metabolismand porphyrias. IV. Pathophysiology of erythyropoietic protoporphyria--diagnosis, care and monitoring of the patient
-
Thunell S, Harper P, Brun A. Porphyrins, porphyrin metabolismand porphyrias. IV. Pathophysiology of erythyropoietic protoporphyria--diagnosis, care and monitoring of the patient. Scand J Clin Lab Invest 2000; 60: 581-604
-
(2000)
Scand J Clin Lab Invest
, vol.60
, pp. 581-604
-
-
Thunell, S.1
Harper, P.2
Brun, A.3
-
16
-
-
35348885053
-
Late presentation of erythropoietic protoporphyria: Case report and genetic analysis of family members
-
Berroeta L, Man I, Goudie DR, Whatley SD, Elder GH, Ibbotson SH. Late presentation of erythropoietic protoporphyria: case report and genetic analysis of family members. Br J Dermatol 2007; 157: 1030-1031
-
(2007)
Br J Dermatol
, vol.157
, pp. 1030-1031
-
-
Berroeta, L.1
Man, I.2
Goudie, D.R.3
Whatley, S.D.4
Elder, G.H.5
Ibbotson, S.H.6
-
18
-
-
0022525866
-
Molecular and cellular mechanisms of porphyrin photosensitization
-
Poh-Fitzpatrick MB. Molecular and cellular mechanisms of porphyrin photosensitization. Photodermatol 1986; 3: 148-157
-
(1986)
Photodermatol
, vol.3
, pp. 148-157
-
-
Poh-Fitzpatrick, M.B.1
-
19
-
-
33747033382
-
Erythropoietic protoporphyria in the U.K.: Clinical features and effect on quality of life
-
Holme SA, Anstey AV, Finlay AY, Elder GH, Badminton MN. Erythropoietic protoporphyria in the U.K.: clinical features and effect on quality of life. Br J Dermatol 2006; 155: 574-581
-
(2006)
Br J Dermatol
, vol.155
, pp. 574-581
-
-
Holme, S.A.1
Anstey, A.V.2
Finlay, A.Y.3
Elder, G.H.4
Badminton, M.N.5
-
20
-
-
0024787213
-
Interaction of hemopexin, albumin and liver fatty acid-binding protein with protoporphyrin
-
Knobler E, Poh-Fitzpatrick MB, Kravetz D, Vincent WR, Muller-Eberhard U, Vincent SH. Interaction of hemopexin, albumin and liver fatty acid-binding protein with protoporphyrin. Hepatology 1989; 10: 995-997
-
(1989)
Hepatology
, vol.10
, pp. 995-997
-
-
Knobler, E.1
Poh-Fitzpatrick, M.B.2
Kravetz, D.3
Vincent, W.R.4
Muller-Eberhard, U.5
Vincent, S.H.6
-
21
-
-
0025924426
-
Gallstones in children
-
Todd DJ. Gallstones in children. Am J Dis Child 1991; 145: 971-972
-
(1991)
Am J Dis Child
, vol.145
, pp. 971-972
-
-
Todd, D.J.1
-
22
-
-
0022643122
-
Fatal liver failure in protoporphyria. Synergism between ethanol excess and the genetic defect
-
Bonkovsky HL, Schned AR. Fatal liver failure in protoporphyria. Synergism between ethanol excess and the genetic defect. Gastroenterology 1986; 90: 191-201
-
(1986)
Gastroenterology
, vol.90
, pp. 191-201
-
-
Bonkovsky, H.L.1
Schned, A.R.2
-
23
-
-
0025935128
-
Severe liver disease in protoporphyria
-
Frank M, Doss MO. Severe liver disease in protoporphyria. Curr Probl Dermatol 1991; 20: 160-167
-
(1991)
Curr Probl Dermatol
, vol.20
, pp. 160-167
-
-
Frank, M.1
Doss, M.O.2
-
24
-
-
44449157828
-
Liver disease in erythropoietic protoporphyria: Insights and implications for management
-
Anstey AV, Hift RJ. Liver disease in erythropoietic protoporphyria: insights and implications for management. Postgrad Med J 2007; 83: 739-748
-
(2007)
Postgrad Med J
, vol.83
, pp. 739-748
-
-
Anstey, A.V.1
Hift, R.J.2
-
25
-
-
34249099684
-
Use of extracorporeal albumin dialysis for erythropoietic protoporphyria
-
McGuire BM, Bloomer JR. Use of extracorporeal albumin dialysis for erythropoietic protoporphyria. Liver Transpl 2007; 13: 639-640
-
(2007)
Liver Transpl
, vol.13
, pp. 639-640
-
-
McGuire, B.M.1
Bloomer, J.R.2
-
26
-
-
45749152114
-
Liver transplantation for erythropoietic protoporphyria with hepatic failure: A case report
-
Zhang F, Lu L, Qian X, Pu LY, Li GQ, Wang XH. Liver transplantation for erythropoietic protoporphyria with hepatic failure: a case report. Transplant Proc 2008; 40: 1774-1776
-
(2008)
Transplant Proc
, vol.40
, pp. 1774-1776
-
-
Zhang, F.1
Lu, L.2
Qian, X.3
Pu, L.Y.4
Li, G.Q.5
Wang, X.H.6
-
27
-
-
0023749913
-
Liver transplantation for protoporphyria. Evidence for the predominant role of the erythropoietic tissue in protoporphy-rin overproduction
-
Samuel D, Boboc B, Bernuau J, Bismuth H, Benhamou JP. Liver transplantation for protoporphyria. Evidence for the predominant role of the erythropoietic tissue in protoporphy-rin overproduction. Gastroenterology 1988; 95: 816-819
-
(1988)
Gastroenterology
, vol.95
, pp. 816-819
-
-
Samuel, D.1
Boboc, B.2
Bernuau, J.3
Bismuth, H.4
Benhamou, J.P.5
-
28
-
-
0023712729
-
The effect of liver transplantation in a 13-year-old boy with erythropoietic protoporphyria
-
Polson RJ, Lim CK, Rolles K, Calne RY, Williams R. The effect of liver transplantation in a 13-year-old boy with erythropoietic protoporphyria. Transplantation 1988; 46: 386-389
-
(1988)
Transplantation
, vol.46
, pp. 386-389
-
-
Polson, R.J.1
Lim, C.K.2
Rolles, K.3
Calne, R.Y.4
Williams, R.5
-
29
-
-
0024338232
-
Liver transplantation in a patient with protoporphyria
-
Bloomer JR, Weimer MK, Bossenmaier IC, Snover DC, Payne WD, Ascher NL. Liver transplantation in a patient with protoporphyria. Gastroenterology 1989; 97: 188-194
-
(1989)
Gastroenterology
, vol.97
, pp. 188-194
-
-
Bloomer, J.R.1
Weimer, M.K.2
Bossenmaier, I.C.3
Snover, D.C.4
Payne, W.D.5
Ascher, N.L.6
-
30
-
-
0024430391
-
Erythrohepatic protoporphyria with rapidly progressing liver cirrhosis
-
Wagner S, Doss MO, Wittekind C, Bäcker U, Meessen D, Schmidt FW. [Erythrohepatic protoporphyria with rapidly progressing liver cirrhosis] Dtsch Med Wochenschr 1989; 114: 1837-1841
-
(1989)
Dtsch Med Wochenschr
, vol.114
, pp. 1837-1841
-
-
Wagner, S.1
Doss, M.O.2
Wittekind, C.3
Bäcker, U.4
Meessen, D.5
Schmidt, F.W.6
-
31
-
-
0026676987
-
Liver transplantation for erythropoietic protoporphyria. Report of a new case with subsequent medium-term followup
-
Mion FB, Faure JL, Berger F, McGregor B, Perrot H, Paliard P. Liver transplantation for erythropoietic protoporphyria. Report of a new case with subsequent medium-term followup. J Hepatol 1992; 16: 203-207
-
(1992)
J Hepatol
, vol.16
, pp. 203-207
-
-
Mion, F.B.1
Faure, J.L.2
Berger, F.3
McGregor, B.4
Perrot, H.5
Paliard, P.6
-
32
-
-
0029122123
-
Autosomal recessive erythropoietic protoporphyria: A syndrome of severe photosensitivity and liver failure
-
Sarkany RP, Cox TM. Autosomal recessive erythropoietic protoporphyria: a syndrome of severe photosensitivity and liver failure. QJM 1995; 88: 541-549
-
(1995)
QJM
, vol.88
, pp. 541-549
-
-
Sarkany, R.P.1
Cox, T.M.2
-
33
-
-
0029335308
-
Liver cirrhosis in protoporphyria: Bile acid therapy and liver transplantation
-
Frank M, Doss MO. [Liver cirrhosis in protoporphyria: bile acid therapy and liver transplantation] Z Gastroenterol 1995; 33: 399-403
-
(1995)
Z Gastroenterol
, vol.33
, pp. 399-403
-
-
Frank, M.1
Doss, M.O.2
-
34
-
-
0037181417
-
Treatment of recurrent allograft dysfunction with intravenous hematin after liver transplantation for erythropoietic protoporphyria
-
Dellon ES, Szczepiorkowski ZM, Dzik WH, Graeme-Cook F, Ades A, Bloomer JR, Cosimi AB, Chung RT. Treatment of recurrent allograft dysfunction with intravenous hematin after liver transplantation for erythropoietic protoporphyria. Transplantation 2002; 73: 911-915
-
(2002)
Transplantation
, vol.73
, pp. 911-915
-
-
Dellon, E.S.1
Szczepiorkowski, Z.M.2
Dzik, W.H.3
Graeme-Cook, F.4
Ades, A.5
Bloomer, J.R.6
Cosimi, A.B.7
Chung, R.T.8
-
35
-
-
0037083764
-
Benefits of chronic plasmapheresis and intravenous hemealbumin in erythropoietic protoporphyria after orthotopic liver transplantation
-
Do KD, Banner BF, Katz E, Szymanski IO, Bonkovsky HL. Benefits of chronic plasmapheresis and intravenous hemealbumin in erythropoietic protoporphyria after orthotopic liver transplantation. Transplantation 2002; 73: 469-472
-
(2002)
Transplantation
, vol.73
, pp. 469-472
-
-
Do, K.D.1
Banner, B.F.2
Katz, E.3
Szymanski, I.O.4
Bonkovsky, H.L.5
-
36
-
-
0026741509
-
Liver transplantation in erythrohepatic protoporphyria
-
Steinmüller T, Doss MO, Steffen R, Blumhardt G, Bechstein WO, Frank M, Sieg I, Kretschmar R, Neuhaus P. [Liver transplantation in erythrohepatic protoporphyria] Dtsch Med Wochenschr 1992; 117: 1097-1102
-
(1992)
Dtsch Med Wochenschr
, vol.117
, pp. 1097-1102
-
-
Steinmüller, T.1
Doss, M.O.2
Steffen, R.3
Blumhardt, G.4
Bechstein, W.O.5
Frank, M.6
Sieg, I.7
Kretschmar, R.8
Neuhaus, P.9
-
37
-
-
0029739647
-
Liver failure in erythropoietic protoporphyria associated with choledocholithiasis and severe post-transplantation polyneuropathy
-
Lock G, Holstege A, Mueller AR, Christe W, Doss MO, Schölmerich J, Neuhaus P. Liver failure in erythropoietic protoporphyria associated with choledocholithiasis and severe post-transplantation polyneuropathy. Liver 1996; 16: 211-217
-
(1996)
Liver
, vol.16
, pp. 211-217
-
-
Lock, G.1
Holstege, A.2
Mueller, A.R.3
Christe, W.4
Doss, M.O.5
Schölmerich, J.6
Neuhaus, P.7
-
38
-
-
0029968781
-
Recurrent hepatic allograft injury in erythropoietic protoporphyria
-
de Torres I, Demetris AJ, Randhawa PS. Recurrent hepatic allograft injury in erythropoietic protoporphyria. Transplantation 1996; 61: 1412-1413
-
(1996)
Transplantation
, vol.61
, pp. 1412-1413
-
-
de Torres, I.1
Demetris, A.J.2
Randhawa, P.S.3
-
39
-
-
0033608752
-
The value of intravenous heme-albumin and plasmapheresis in reducing postoperative complications of orthotopic liver transplantation for erythropoietic protoporphyria
-
Reichheld JH, Katz E, Banner BF, Szymanski IO, Saltzman JR, Bonkovsky HL. The value of intravenous heme-albumin and plasmapheresis in reducing postoperative complications of orthotopic liver transplantation for erythropoietic protoporphyria. Transplantation 1999; 67: 922-928
-
(1999)
Transplantation
, vol.67
, pp. 922-928
-
-
Reichheld, J.H.1
Katz, E.2
Banner, B.F.3
Szymanski, I.O.4
Saltzman, J.R.5
Bonkovsky, H.L.6
-
40
-
-
0032923465
-
Long-term follow-up after liver transplantation for erythropoietic protoporphyria
-
Meerman L, Haagsma EB, Gouw AS, Slooff MJ, Jansen PL. Long-term follow-up after liver transplantation for erythropoietic protoporphyria. Eur J Gastroenterol Hepatol 1999; 11: 431-438
-
(1999)
Eur J Gastroenterol Hepatol
, vol.11
, pp. 431-438
-
-
Meerman, L.1
Haagsma, E.B.2
Gouw, A.S.3
Slooff, M.J.4
Jansen, P.L.5
-
41
-
-
0032856179
-
Photosensitivity and perioperative polyneuropathy complicating orthotopic liver transplantation in a patient with erythropoietic protoporphyria
-
Nguyen L, Blust M, Bailin M, Melendez L, Raines DE. Photosensitivity and perioperative polyneuropathy complicating orthotopic liver transplantation in a patient with erythropoietic protoporphyria. Anesthesiology 1999; 91: 1173-1175
-
(1999)
Anesthesiology
, vol.91
, pp. 1173-1175
-
-
Nguyen, L.1
Blust, M.2
Bailin, M.3
Melendez, L.4
Raines, D.E.5
-
42
-
-
0033542530
-
Severe liver failure in erythropoietic protoporphyria. A report of a case treated by liver transplantation
-
Jiménez-Sáenz M, Caunedo-Alvarez A, Rojas M, Mata M, Villar JL, Piñar A, Herrerías-Gutiérrez J. [Severe liver failure in erythropoietic protoporphyria. A report of a case treated by liver transplantation] Med Clin (Barc) 1999; 113: 176-179
-
(1999)
Med Clin (Barc)
, vol.113
, pp. 176-179
-
-
Jiménez-Sáenz, M.1
Caunedo-Alvarez, A.2
Rojas, M.3
Mata, M.4
Villar, J.L.5
Piñar, A.6
Herrerías-Gutiérrez, J.7
-
43
-
-
0028334778
-
Hepatic complications of erythropoietic protoporphyria
-
Sarkany RP, Norris PG. Hepatic complications of erythropoietic protoporphyria. Br J Dermatol 1994; 130: 258-259
-
(1994)
Br J Dermatol
, vol.130
, pp. 258-259
-
-
Sarkany, R.P.1
Norris, P.G.2
-
44
-
-
0022534170
-
Hepatic disease in erythropoietic protoporphyria
-
Mooyaart BR, de Jong GM, van der Veen S, Driessen LH, Beukeveld GJ, Grond J, Gips CH. Hepatic disease in erythropoietic protoporphyria. Dermatologica 1986; 173: 120-130
-
(1986)
Dermatologica
, vol.173
, pp. 120-130
-
-
Mooyaart, B.R.1
de Jong, G.M.2
van der Veen, S.3
Driessen, L.H.4
Beukeveld, G.J.5
Grond, J.6
Gips, C.H.7
-
45
-
-
30444434611
-
Liver transplantation for erythropoietic protoporphyria liver disease
-
McGuire BM, Bonkovsky HL, Carithers RL Jr, Chung RT, Goldstein LI, Lake JR, Lok AS, Potter CJ, Rand E, Voigt MD, Davis PR, Bloomer JR. Liver transplantation for erythropoietic protoporphyria liver disease. Liver Transpl 2005; 11: 1590-1596
-
(2005)
Liver Transpl
, vol.11
, pp. 1590-1596
-
-
McGuire, B.M.1
Bonkovsky, H.L.2
Carithers Jr., R.L.3
Chung, R.T.4
Goldstein, L.I.5
Lake, J.R.6
Lok, A.S.7
Potter, C.J.8
Rand, E.9
Voigt, M.D.10
Davis, P.R.11
Bloomer, J.R.12
-
46
-
-
0035668408
-
Liver cirrhosis in erythropoietic protoporphyria: Improvement of liver function with ursodeoxycholic acid
-
Pirlich M, Lochs H, Schmidt HH. Liver cirrhosis in erythropoietic protoporphyria: improvement of liver function with ursodeoxycholic acid. Am J Gastroenterol 2001; 96: 3468-3469
-
(2001)
Am J Gastroenterol
, vol.96
, pp. 3468-3469
-
-
Pirlich, M.1
Lochs, H.2
Schmidt, H.H.3
-
47
-
-
0036725044
-
Ursodeoxycholic acid in cholestatic liver disease: Mechanisms of action and therapeutic use revisited
-
Paumgartner G, Beuers U. Ursodeoxycholic acid in cholestatic liver disease: mechanisms of action and therapeutic use revisited. Hepatology 2002; 36: 525-531
-
(2002)
Hepatology
, vol.36
, pp. 525-531
-
-
Paumgartner, G.1
Beuers, U.2
-
49
-
-
0021038558
-
Transfusion therapy for erythropoietic protoporphyria
-
Dobozy A, Csató M, Siklósi C, Simon N. Transfusion therapy for erythropoietic protoporphyria. Br J Dermatol 1983; 109: 571-576
-
(1983)
Br J Dermatol
, vol.109
, pp. 571-576
-
-
Dobozy, A.1
Csató, M.2
Siklósi, C.3
Simon, N.4
-
50
-
-
0022654509
-
Iron therapy for hepatic dysfunction in erythropoietic protoporphyria
-
Gordeuk VR, Brittenham GM, Hawkins CW, Mukhtar H, Bickers DR. Iron therapy for hepatic dysfunction in erythropoietic protoporphyria. Ann Intern Med 1986; 105: 27-31
-
(1986)
Ann Intern Med
, vol.105
, pp. 27-31
-
-
Gordeuk, V.R.1
Brittenham, G.M.2
Hawkins, C.W.3
Mukhtar, H.4
Bickers, D.R.5
-
51
-
-
34248224192
-
Symptomatic response of erythropoietic protoporphyria to iron supplementation
-
Holme SA, Thomas CL, Whatley SD, Bentley DP, Anstey AV, Badminton MN. Symptomatic response of erythropoietic protoporphyria to iron supplementation. J Am Acad Dermatol 2007; 56: 1070-1072
-
(2007)
J Am Acad Dermatol
, vol.56
, pp. 1070-1072
-
-
Holme, S.A.1
Thomas, C.L.2
Whatley, S.D.3
Bentley, D.P.4
Anstey, A.V.5
Badminton, M.N.6
-
52
-
-
0030462392
-
Hematin therapy in children with protoporphyric liver disease
-
Potter C, Tolaymat N, Bobo R, Sharp H, Rank J, Bloomer J. Hematin therapy in children with protoporphyric liver disease. J Pediatr Gastroenterol Nutr 1996; 23: 402-407
-
(1996)
J Pediatr Gastroenterol Nutr
, vol.23
, pp. 402-407
-
-
Potter, C.1
Tolaymat, N.2
Bobo, R.3
Sharp, H.4
Rank, J.5
Bloomer, J.6
-
53
-
-
0032833890
-
Long-term follow-up after liver transplantation in patients with hepatic iron overload
-
Tung BY, Farrell FJ, McCashland TM, Gish RG, Bacon BR, Keeffe EB, Kowdley KV. Long-term follow-up after liver transplantation in patients with hepatic iron overload. Liver Transpl Surg 1999; 5: 369-374
-
(1999)
Liver Transpl Surg
, vol.5
, pp. 369-374
-
-
Tung, B.Y.1
Farrell, F.J.2
McCashland, T.M.3
Gish, R.G.4
Bacon, B.R.5
Keeffe, E.B.6
Kowdley, K.V.7
-
54
-
-
34248999740
-
Erythropoietic protoporphyria and pretransplantation treatment with nonbiological liver assist devices
-
Eefsen M, Rasmussen A, Wulf HC, Brock A, Hansen BA. Erythropoietic protoporphyria and pretransplantation treatment with nonbiological liver assist devices. Liver Transpl 2007; 13: 655-657
-
(2007)
Liver Transpl
, vol.13
, pp. 655-657
-
-
Eefsen, M.1
Rasmussen, A.2
Wulf, H.C.3
Brock, A.4
Hansen, B.A.5
-
55
-
-
0023853909
-
Fecal protoporphyrin excretion in erythropoietic protoporphyria: Effect of cholestyramine and bile acid feeding
-
McCullough AJ, Barron D, Mullen KD, Petrelli M, Park MC, Mukhtar H, Bickers DR. Fecal protoporphyrin excretion in erythropoietic protoporphyria: effect of cholestyramine and bile acid feeding. Gastroenterology 1988; 94: 177-181
-
(1988)
Gastroenterology
, vol.94
, pp. 177-181
-
-
McCullough, A.J.1
Barron, D.2
Mullen, K.D.3
Petrelli, M.4
Park, M.C.5
Mukhtar, H.6
Bickers, D.R.7
-
56
-
-
4243910889
-
Oral activated charcoal in protoporphyria with liver damage
-
Gorchein A, Chong SK, Mowat AP. Oral activated charcoal in protoporphyria with liver damage. Br J Clin Pharmacol 1989; 27: 703P
-
(1989)
Br J Clin Pharmacol
, vol.27
, pp. 703
-
-
Gorchein, A.1
Chong, S.K.2
Mowat, A.P.3
-
57
-
-
0033055986
-
Liver failure in protoporphyria: Long-term treatment with oral charcoal
-
Gorchein A, Foster GR. Liver failure in protoporphyria: long-term treatment with oral charcoal. Hepatology 1999; 29: 995-996
-
(1999)
Hepatology
, vol.29
, pp. 995-996
-
-
Gorchein, A.1
Foster, G.R.2
-
58
-
-
73349136974
-
Role of free radicals in liver diseases
-
Muriel P. Role of free radicals in liver diseases. Hepatol Int 2009; 3: 526-536
-
(2009)
Hepatol Int
, vol.3
, pp. 526-536
-
-
Muriel, P.1
-
59
-
-
0342545424
-
Apolinario A,Moreno-Otero R. Intrahepatic accumulation of nitrotyrosine in chronic viral hepatitis is associated with histological severity of liver disease
-
García-Monzón C, Majano PL, Zubia I, Sanz P, Apolinario A,Moreno-Otero R. Intrahepatic accumulation of nitrotyrosine in chronic viral hepatitis is associated with histological severity of liver disease. J Hepatol 2000; 32: 331-338
-
(2000)
J Hepatol
, vol.32
, pp. 331-338
-
-
García-Monzón, C.1
Majano, P.L.2
Zubia, I.3
Sanz, P.4
-
60
-
-
0036893739
-
Enhanced intrahepatic inducible nitric oxide synthase expression and nitrotyrosine accumulation in primary biliary cirrhosis and autoimmune hepatitis
-
Sanz-Cameno P, Medina J, García-Buey L, García-Sánchez A, Borque MJ, Martín-Vílchez S, Gamallo C, Jones EA, Moreno-Otero R. Enhanced intrahepatic inducible nitric oxide synthase expression and nitrotyrosine accumulation in primary biliary cirrhosis and autoimmune hepatitis. J Hepatol 2002; 37: 723-729
-
(2002)
J Hepatol
, vol.37
, pp. 723-729
-
-
Sanz-Cameno, P.1
Medina, J.2
García-Buey, L.3
García-Sánchez, A.4
Borque, M.J.5
Martín-Vílchez, S.6
Gamallo, C.7
Jones, E.A.8
Moreno-Otero, R.9
-
61
-
-
1642339441
-
N-Acetyl-cysteine modulates inducible nitric oxide synthase gene expression in human hepatocytes
-
Majano PL, Medina J, Zubía I, Sunyer L, Lara-Pezzi E, Maldonado-Rodríguez A, López-Cabrera M, Moreno-Otero R. N-Acetyl-cysteine modulates inducible nitric oxide synthase gene expression in human hepatocytes. J Hepatol 2004; 40: 632-637
-
(2004)
J Hepatol
, vol.40
, pp. 632-637
-
-
Majano, P.L.1
Medina, J.2
Zubía, I.3
Sunyer, L.4
Lara-Pezzi, E.5
Maldonado-Rodríguez, A.6
López-Cabrera, M.7
Moreno-Otero, R.8
-
62
-
-
28144449739
-
Pathophysiological basis for antioxidant therapy in chronic liver disease
-
Medina J, Moreno-Otero R. Pathophysiological basis for antioxidant therapy in chronic liver disease. Drugs 2005; 65: 2445-2461
-
(2005)
Drugs
, vol.65
, pp. 2445-2461
-
-
Medina, J.1
Moreno-Otero, R.2
-
63
-
-
67649217804
-
N-acetyl cysteine averted liver transplantation in a patient with liver failure caused by erythropoietic protoporphyria
-
Sperl J, Procházková J, Martásek P, Subhanová I, Franková S, Trunecka P, Jirsa M. N-acetyl cysteine averted liver transplantation in a patient with liver failure caused by erythropoietic protoporphyria. Liver Transpl 2009; 15: 352-354
-
(2009)
Liver Transpl
, vol.15
, pp. 352-354
-
-
Sperl, J.1
Procházková, J.2
Martásek, P.3
Subhanová, I.4
Franková, S.5
Trunecka, P.6
Jirsa, M.7
-
64
-
-
51349086909
-
Protection from phototoxic injury during surgery and endoscopy in erythropoietic protoporphyria
-
Wahlin S, Srikanthan N, Hamre B, Harper P, Brun A. Protection from phototoxic injury during surgery and endoscopy in erythropoietic protoporphyria. Liver Transpl 2008; 14: 1340-1346
-
(2008)
Liver Transpl
, vol.14
, pp. 1340-1346
-
-
Wahlin, S.1
Srikanthan, N.2
Hamre, B.3
Harper, P.4
Brun, A.5
-
65
-
-
0028008706
-
Perioperative measures during liver transplantation for erythropoietic protoporphyria
-
Meerman L, Verwer R, Slooff MJ, van Hattum J, Beukeveld GJ, Kleibeuker JH, Haagsma EB. Perioperative measures during liver transplantation for erythropoietic protoporphyria. Transplantation 1994; 57: 155-158
-
(1994)
Transplantation
, vol.57
, pp. 155-158
-
-
Meerman, L.1
Verwer, R.2
Slooff, M.J.3
van Hattum, J.4
Beukeveld, G.J.5
Kleibeuker, J.H.6
Haagsma, E.B.7
|