Porphyrins, porphyrin metabolism and porphyrias. IV. Pathophysiology of erythyropoietic protoporphyria - Diagnosis, care and monitoring of the patient

Scandinavian Journal of Clinical and Laboratory Investigation

Volumn 60, Issue 7, 2000, Pages 581-604

  Thunell, S ^a   Harper, P ^a   Brun, A ^a  

^a KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

Author keywords

Biochemical monitoring; Diagnosis; Erythropoietic protoporphyria; Hepatobiliary disease; Literature review; Pathophysiology; Preventive measures; Therapy

Indexed keywords

PORPHYRIN;

ARTICLE; COMPLEMENT ACTIVATION; ENZYME ACTIVITY; ENZYME DEFICIENCY; ERYTHROPOIETIC PROTOPORPHYRIA; GENETIC PREDISPOSITION; HUMAN; HUMAN CELL; MAST CELL DEGRANULATION; MULTIGENE FAMILY; PATHOPHYSIOLOGY; PATIENT CARE; PATIENT MONITORING; PHOTODERMATOSIS; PORPHYRIA; PRIORITY JOURNAL; SUN EXPOSURE;

HUMANS; PORPHYRIA, HEPATOERYTHROPOIETIC; PORPHYRINS;

EID: 0034523846     PISSN: 00365513     EISSN: None     Source Type: Journal    
DOI: 10.1080/003655100448347     Document Type: Article

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