Erythropoietic protoporphyria in the U.K.: Clinical features and effect on quality of life

British Journal of Dermatology

Volumn 155, Issue 3, 2006, Pages 574-581

  Holme, S A ^a,b   Anstey, A V ^a   Finlay, A Y ^a   Elder, G H ^a   Badminton, M N ^a  

^a CARDIFF UNIVERSITY   (United Kingdom)

^b QUEEN MARGARET HOSPITAL   (United Kingdom)

Author keywords

Clinical features; Erythropoietic protoporphyria; Photosensitivity; Porphyria; Quality of life

Indexed keywords

ACETYLCYSTEINE; ANTIHISTAMINIC AGENT; BETA CAROTENE; PORPHYRIN; REFLECTANT; SUNSCREEN;

ADOLESCENT; ADULT; AGED; ARTICLE; BODY FLUID; BODY FLUID DISCOLORATION; CHILD; CHILDREN DERMATOLOGY LIFE QUALITY INDEX; CHOLELITHIASIS; CHRONIC DISEASE; CLINICAL FEATURE; COHORT ANALYSIS; DERMATOLOGY LIFE QUALITY INDEX; DISEASE DURATION; DISEASE EXACERBATION; DRUG CARCINOGENICITY; DYSPHAGIA; EARLY DIAGNOSIS; EDEMA; ERYTHEMA; ERYTHROPOIETIC PROTOPORPHYRIA; FAMILY HISTORY; FEMALE; GASTROINTESTINAL SYMPTOM; HUMAN; LIVER FAILURE; MAJOR CLINICAL STUDY; MALE; ONSET AGE; PAIN; PHOTOSENSITIVITY; PHOTOTHERAPY; PREGNANCY; PRIORITY JOURNAL; PROTECTIVE CLOTHING; QUALITY OF LIFE; QUESTIONNAIRE; RARE DISEASE; RETINA DISEASE; SKIN DEFECT; SKIN DISCOLORATION; SOCIAL DISABILITY; SUN EXPOSURE; UNITED KINGDOM; WIND; WINTER;

ADOLESCENT; ADULT; AGE OF ONSET; AGED; AGED, 80 AND OVER; CHILD; CHILD, PRESCHOOL; CROSS-SECTIONAL STUDIES; FEMALE; HEALTH STATUS INDICATORS; HUMANS; MALE; MIDDLE AGED; PHOTOSENSITIVITY DISORDERS; PORPHYRINS; PROTOPORPHYRIA, ERYTHROPOIETIC; QUALITY OF LIFE; SEVERITY OF ILLNESS INDEX; SOCIOECONOMIC FACTORS; SUNLIGHT;

EID: 33747033382     PISSN: 00070963     EISSN: 13652133     Source Type: Journal    
DOI: 10.1111/j.1365-2133.2006.07472.x     Document Type: Article

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