-
1
-
-
70350279315
-
Atypical hemolytic-uremic syndrome
-
Noris M, Remuzzi G. Atypical hemolytic-uremic syndrome. N Engl J Med 2009 361 (17) 1676-1687
-
(2009)
N Engl J Med
, vol.361
, Issue.17
, pp. 1676-1687
-
-
Noris, M.1
Remuzzi, G.2
-
2
-
-
68049123090
-
Autoimmune forms of thrombotic microangiopathy and membranoproliferative glomerulonephritis: Indications for a disease spectrum and common pathogenic principles
-
Skerka C, Licht C, Mengel M et al. Autoimmune forms of thrombotic microangiopathy and membranoproliferative glomerulonephritis: indications for a disease spectrum and common pathogenic principles. Mol Immunol 2009 46 (14) 2801-2807
-
(2009)
Mol Immunol
, vol.46
, Issue.14
, pp. 2801-2807
-
-
Skerka, C.1
Licht, C.2
Mengel, M.3
-
3
-
-
38949155911
-
Factor H autoantibodies in atypical hemolytic uremic syndrome correlate with CFHR1/CFHR3 deficiency
-
Józsi M, Licht C, Strobel S et al. Factor H autoantibodies in atypical hemolytic uremic syndrome correlate with CFHR1/CFHR3 deficiency. Blood 2008 111 (3) 1512-1514
-
(2008)
Blood
, vol.111
, Issue.3
, pp. 1512-1514
-
-
Józsi, M.1
Licht, C.2
Strobel, S.3
-
4
-
-
67650508077
-
The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome
-
Dragon-Durey M A., Blanc C, Marliot F et al. The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome. J Med Genet 2009 46 (7) 447-450
-
(2009)
J Med Genet
, vol.46
, Issue.7
, pp. 447-450
-
-
Dragon-Durey, M.A.1
Blanc, C.2
Marliot, F.3
-
5
-
-
76949087440
-
Characterization of complement factor H-related (CFHR) proteins in plasma reveals novel genetic variations of CFHR1 associated with atypical hemolytic uremic syndrome
-
Abarrategui-Garrido C, Martnez-Barricarte R, López-Trascasa M, de Córdoba S R., Snchez-Corral P. Characterization of complement factor H-related (CFHR) proteins in plasma reveals novel genetic variations of CFHR1 associated with atypical hemolytic uremic syndrome. Blood 2009 114 (19) 4261-4271
-
(2009)
Blood
, vol.114
, Issue.19
, pp. 4261-4271
-
-
Abarrategui-Garrido, C.1
Martnez-Barricarte, R.2
López-Trascasa, M.3
De Córdoba, S.R.4
Snchez-Corral, P.5
-
6
-
-
34047200899
-
Deletion of complement factor H-related genes CFHR1 and CFHR3 is associated with atypical hemolytic uremic syndrome
-
Zipfel P F., Edey M, Heinen S et al. Deletion of complement factor H-related genes CFHR1 and CFHR3 is associated with atypical hemolytic uremic syndrome. PLoS Genet 2007 3 (3) e41
-
(2007)
PLoS Genet
, vol.3
, Issue.3
-
-
Zipfel, P.F.1
Edey, M.2
Heinen, S.3
-
7
-
-
20544437666
-
Anti-factor H autoantibodies associated with atypical hemolytic uremic syndrome
-
Dragon-Durey M A., Loirat C, Cloarec S et al. Anti-factor H autoantibodies associated with atypical hemolytic uremic syndrome. J Am Soc Nephrol 2005 16 (2) 555-563
-
(2005)
J Am Soc Nephrol
, vol.16
, Issue.2
, pp. 555-563
-
-
Dragon-Durey, M.A.1
Loirat, C.2
Cloarec, S.3
-
8
-
-
70350448229
-
Atypical hemolytic uremic syndrome associated with complement factor H autoantibodies and CFHR1/CFHR3 deficiency
-
Lee B H., Kwak S H., Shin J I. et al. Atypical hemolytic uremic syndrome associated with complement factor H autoantibodies and CFHR1/CFHR3 deficiency. Pediatr Res 2009 66 (3) 336-340
-
(2009)
Pediatr Res
, vol.66
, Issue.3
, pp. 336-340
-
-
Lee, B.H.1
Kwak, S.H.2
Shin, J.I.3
-
9
-
-
65249156546
-
Anti-factor H autoantibodies in a fifth renal transplant recipient with atypical hemolytic and uremic syndrome
-
Le Quintrec M, Zuber J, Noel L H. et al. Anti-factor H autoantibodies in a fifth renal transplant recipient with atypical hemolytic and uremic syndrome. Am J Transplant 2009 9 (5) 1223-1229
-
(2009)
Am J Transplant
, vol.9
, Issue.5
, pp. 1223-1229
-
-
Le Quintrec, M.1
Zuber, J.2
Noel, L.H.3
-
10
-
-
53749084348
-
Complement and the atypical hemolytic uremic syndrome in children
-
Loirat C, Noris M, Frémeaux-Bacchi V. Complement and the atypical hemolytic uremic syndrome in children. Pediatr Nephrol 2008 23 (11) 1957-1972
-
(2008)
Pediatr Nephrol
, vol.23
, Issue.11
, pp. 1957-1972
-
-
Loirat, C.1
Noris, M.2
Frémeaux-Bacchi, V.3
-
11
-
-
72949096309
-
Functional analyses indicate a pathogenic role of factor H autoantibodies in atypical haemolytic uraemic syndrome
-
Strobel S, Hoyer P F., Mache C J. et al. Functional analyses indicate a pathogenic role of factor H autoantibodies in atypical haemolytic uraemic syndrome. Nephrol Dial Transplant 2010 25 (1) 136-144
-
(2010)
Nephrol Dial Transplant
, vol.25
, Issue.1
, pp. 136-144
-
-
Strobel, S.1
Hoyer, P.F.2
MacHe, C.J.3
-
12
-
-
34548853385
-
Anti factor H autoantibodies block C-terminal recognition function of factor H in hemolytic uremic syndrome
-
Józsi M, Strobel S, Dahse H M. et al. Anti factor H autoantibodies block C-terminal recognition function of factor H in hemolytic uremic syndrome. Blood 2007 110 (5) 1516-1518
-
(2007)
Blood
, vol.110
, Issue.5
, pp. 1516-1518
-
-
Józsi, M.1
Strobel, S.2
Dahse, H.M.3
-
13
-
-
33645851021
-
The C-terminus of complement regulator factor H mediates target recognition: Evidence for a compact conformation of the native protein
-
Oppermann M, Manuelian T, Józsi M et al. The C-terminus of complement regulator factor H mediates target recognition: evidence for a compact conformation of the native protein. Clin Exp Immunol 2006 144 (2) 342-352
-
(2006)
Clin Exp Immunol
, vol.144
, Issue.2
, pp. 342-352
-
-
Oppermann, M.1
Manuelian, T.2
Józsi, M.3
-
14
-
-
57649230771
-
Complement factor H related proteins in immune diseases
-
Skerka C, Zipfel P F. Complement factor H related proteins in immune diseases. Vaccine 2008 26 (Suppl 8) I9-I14
-
(2008)
Vaccine
, vol.26
, Issue.SUPPL. 8
-
-
Skerka, C.1
Zipfel, P.F.2
-
15
-
-
0033033505
-
FHL-1/reconectin: A human complement and immune regulator with cell-adhesive function
-
Zipfel P F., Skerka C. FHL-1/reconectin: a human complement and immune regulator with cell-adhesive function. Immunol Today 1999 20 (3) 135-140
-
(1999)
Immunol Today
, vol.20
, Issue.3
, pp. 135-140
-
-
Zipfel, P.F.1
Skerka, C.2
-
16
-
-
0026047501
-
Molecular cloning of a human serum protein structurally related to complement factor H
-
Skerka C, Horstmann R D., Zipfel P F. Molecular cloning of a human serum protein structurally related to complement factor H. J Biol Chem 1991 266 (18) 12015-12020
-
(1991)
J Biol Chem
, vol.266
, Issue.18
, pp. 12015-12020
-
-
Skerka, C.1
Horstmann, R.D.2
Zipfel, P.F.3
-
17
-
-
0027450002
-
A novel short consensus repeat-containing molecule is related to human complement factor H
-
Skerka C, Kühn S, Günther K, Lingelbach K, Zipfel P F. A novel short consensus repeat-containing molecule is related to human complement factor H. J Biol Chem 1993 268 (4) 2904-2908
-
(1993)
J Biol Chem
, vol.268
, Issue.4
, pp. 2904-2908
-
-
Skerka, C.1
Kühn, S.2
Günther, K.3
Lingelbach, K.4
Zipfel, P.F.5
-
18
-
-
0031054530
-
The human factor H-related protein 4 (FHR-4). A novel short consensus repeat-containing protein is associated with human triglyceride-rich lipoproteins
-
Skerka C, Hellwage J, Weber W et al. The human factor H-related protein 4 (FHR-4). A novel short consensus repeat-containing protein is associated with human triglyceride-rich lipoproteins. J Biol Chem 1997 272 (9) 5627-5634
-
(1997)
J Biol Chem
, vol.272
, Issue.9
, pp. 5627-5634
-
-
Skerka, C.1
Hellwage, J.2
Weber, W.3
-
19
-
-
14944365484
-
FHR-4A: A new factor H-related protein is encoded by the human FHR-4 gene
-
Józsi M, Richter H, Löschmann I et al. FHR-4A: a new factor H-related protein is encoded by the human FHR-4 gene. Eur J Hum Genet 2005 13 (3) 321-329
-
(2005)
Eur J Hum Genet
, vol.13
, Issue.3
, pp. 321-329
-
-
Józsi, M.1
Richter, H.2
Löschmann, I.3
-
20
-
-
0026560005
-
Two additional human serum proteins structurally related to complement factor H. Evidence for a family of factor H-related genes
-
Skerka C, Timmann C, Horstmann R D., Zipfel P F. Two additional human serum proteins structurally related to complement factor H. Evidence for a family of factor H-related genes. J Immunol 1992 148 (10) 3313-3318
-
(1992)
J Immunol
, vol.148
, Issue.10
, pp. 3313-3318
-
-
Skerka, C.1
Timmann, C.2
Horstmann, R.D.3
Zipfel, P.F.4
-
21
-
-
0035794141
-
Human factor H-related protein 5 (FHR-5). A new complement-associated protein
-
McRae J L., Cowan P J., Power D A. et al. Human factor H-related protein 5 (FHR-5). A new complement-associated protein. J Biol Chem 2001 276 (9) 6747-6754
-
(2001)
J Biol Chem
, vol.276
, Issue.9
, pp. 6747-6754
-
-
McRae, J.L.1
Cowan, P.J.2
Power, D.A.3
-
22
-
-
33750855444
-
Atypical haemolytic uraemic syndrome associated with a hybrid complement gene
-
Venables J P., Strain L, Routledge D et al. Atypical haemolytic uraemic syndrome associated with a hybrid complement gene. PLoS Med 2006 3 (10) e431
-
(2006)
PLoS Med
, vol.3
, Issue.10
-
-
Venables, J.P.1
Strain, L.2
Routledge, D.3
-
23
-
-
70349441306
-
Factor H-related protein 1 (CFHR-1) inhibits complement C5 convertase activity and terminal complex formation
-
Heinen S, Hartmann A, Lauer N et al. Factor H-related protein 1 (CFHR-1) inhibits complement C5 convertase activity and terminal complex formation. Blood 2009 114 (12) 2439-2447
-
(2009)
Blood
, vol.114
, Issue.12
, pp. 2439-2447
-
-
Heinen, S.1
Hartmann, A.2
Lauer, N.3
-
24
-
-
70349437186
-
Complement regulators and inhibitory proteins
-
Zipfel P F., Skerka C. Complement regulators and inhibitory proteins. Nat Rev Immunol 2009 9 (10) 729-740
-
(2009)
Nat Rev Immunol
, vol.9
, Issue.10
, pp. 729-740
-
-
Zipfel, P.F.1
Skerka, C.2
-
25
-
-
67349259594
-
A novel mutation in the complement regulator clusterin in recurrent hemolytic uremic syndrome
-
Ståhl A L., Kristoffersson A, Olin A I. et al. A novel mutation in the complement regulator clusterin in recurrent hemolytic uremic syndrome. Mol Immunol 2009 46 (11-12) 2236-2243
-
(2009)
Mol Immunol
, vol.46
, Issue.1112
, pp. 2236-2243
-
-
Ståhl, A.L.1
Kristoffersson, A.2
Olin, A.I.3
|