Familial predisposition to adrenocortical tumors: Clinical and biological features and management strategies

Best Practice and Research: Clinical Endocrinology and Metabolism

Volumn 24, Issue 3, 2010, Pages 477-490

  Ribeiro, Raul C ^a,b   Pinto, Emilia M ^a   Zambetti, Gerard P ^a,b  

^a ST JUDE CHILDREN S RESEARCH HOSPITAL   (United States)

^b UNIVERSITY OF TENNESSEE COLLEGE OF MEDICINE   (United States)

Author keywords

Adrenocortical tumors; Familial cancer syndromes; Management of adrenocortical tumors

Indexed keywords

AMINOGLUTETHIMIDE; ANTIHYPERTENSIVE AGENT; ANTINEOPLASTIC AGENT; CARBOPLATIN; CISPLATIN; CYCLOPHOSPHAMIDE; DOXORUBICIN; ETOPOSIDE; FLUOROURACIL; KETOCONAZOLE; MITOTANE; PROTEIN P53; SOMATOMEDIN C RECEPTOR BLOCKING AGENT; STREPTOZOCIN; UNCLASSIFIED DRUG;

ABDOMINAL PAIN; ADENOMATOUS POLYP; ADRENAL CORTEX TUMOR; ATAXIA; BECKWITH WIEDEMANN SYNDROME; CARNEY COMPLEX; CLINICAL EVALUATION; CLINICAL FEATURE; CLINICAL TRIAL; DEPRESSION; DIARRHEA; DISEASE PREDISPOSITION; FAMILIAL CANCER; GENE MUTATION; HEREDITY; HUMAN; HYPERCORTISOLISM; LETHARGY; MULTIPLE ENDOCRINE NEOPLASIA; NAUSEA; OUTCOME ASSESSMENT; PATHOGENESIS; PROGNOSIS; REVIEW; SOMNOLENCE; SURGICAL TECHNIQUE; VERTIGO; VOMITING;

ADOLESCENT; ADRENAL CORTEX NEOPLASMS; ADRENOCORTICAL CARCINOMA; CHILD; CHILD, PRESCHOOL; FEMALE; GENES, P53; GENETIC PREDISPOSITION TO DISEASE; HUMANS; LI-FRAUMENI SYNDROME; MALE;

EID: 77956603309     PISSN: 1521690X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.beem.2010.03.002     Document Type: Review

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