Mice with DNA repair gene Ercc1 deficiency in a neural crest lineage are a model for late-onset Hirschsprung disease

DNA Repair

Volumn 9, Issue 6, 2010, Pages 653-660

  Selfridge, Jim ^a   Song, Liang ^b   Brownstein, David G ^c   Melton, David W ^b  

^a UNIVERSITY OF EDINBURGH   (United Kingdom)

^b UNIVERSITY OF EDINBURGH   (United Kingdom)

^c UNIVERSITY OF EDINBURGH   (United Kingdom)

Author keywords

Colonic obstruction; DNA damage; Enteric nervous system; Melanocytes; Nucleotide excision repair

Indexed keywords

CRE RECOMBINASE; EXCISION REPAIR CROSS COMPLEMENTING PROTEIN 1; MONOPHENOL MONOOXYGENASE; DNA BINDING PROTEIN; ENDONUCLEASE; ERCC1 PROTEIN, MOUSE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL LINEAGE; CHOLINERGIC SYSTEM; COLON OBSTRUCTION; CONTROLLED STUDY; DISEASE PREDISPOSITION; DNA REPAIR; EXCISION REPAIR; GENE EXPRESSION; HIRSCHSPRUNG DISEASE; INTESTINE INNERVATION; MELANOCYTE; MELANOMA; MOUSE; NEURAL CREST CELL; NONHUMAN; PARASYMPATHETIC GANGLION; PATHOGENESIS; PRIORITY JOURNAL; PROMOTER REGION; STOMACH MOTILITY; ULTRAVIOLET IRRADIATION; ANIMAL; ANTIBODY SPECIFICITY; DEFICIENCY; DISEASE MODEL; GENE INACTIVATION; GENETICS; HUMAN; METABOLISM; NEURAL CREST; PATHOLOGY; RADIATION RESPONSE; ULTRAVIOLET RADIATION;

ANIMALS; CELL LINEAGE; DISEASE MODELS, ANIMAL; DNA REPAIR; DNA-BINDING PROTEINS; ENDONUCLEASES; GENE KNOCKOUT TECHNIQUES; HIRSCHSPRUNG DISEASE; HUMANS; MELANOCYTES; MICE; NEURAL CREST; ORGAN SPECIFICITY; PARASYMPATHETIC NERVOUS SYSTEM; ULTRAVIOLET RAYS;

ANIMALIA; MUS;

EID: 77952671170     PISSN: 15687864     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.dnarep.2010.02.018     Document Type: Article

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