Lysosomal storage of oligosaccharide and glycosphingolipid in imino sugar treated cells

Glycoconjugate Journal

Volumn 27, Issue 3, 2010, Pages 297-308

  Boomkamp, Stephanie D ^a   Rountree, J S Shane ^a,b   Neville, David C A ^a   Dwek, Raymond A ^a   Fleet, George W J ^b   Butters, Terry D ^a  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b UNIVERSITY OF OXFORD   (United Kingdom)

Author keywords

Fluorescence labelling; Gangliosidoses; Hexosaminidase inhibition; HPLC analysis

Indexed keywords

ALPHA GLUCOSIDASE; ASPARAGINE LINKED OLIGOSACCHARIDE; BETA GALACTOSIDASE; BETA N ACETYLHEXOSAMINIDASE; CXCL16 CHEMOKINE; EOTAXIN 2; GANGLIOSIDE GM2; GANGLIOTRIGLYCOSYLCERAMIDE; GLYCOCONJUGATE; GLYCOSPHINGOLIPID; IMINOSUGAR; INTERLEUKIN 12P70; INTERLEUKIN 1ALPHA; INTERLEUKIN 1BETA; INTERLEUKIN 4; INTERLEUKIN 9; MACROPHAGE INFLAMMATORY PROTEIN 1ALPHA; MIGLUSTAT; N ACETYLGALACTOSAMINE; N ACETYLGLUCOSAMINE; OLIGOSACCHARIDE; TUMOR NECROSIS FACTOR ALPHA; TUMOR NECROSIS FACTOR RECEPTOR 1; TUMOR NECROSIS FACTOR RECEPTOR 2; UNCLASSIFIED DRUG;

ANIMAL CELL; APOPTOSIS; ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; ENZYME KINETICS; FLUORESCENCE IMAGING; GANGLIOSIDOSIS; GLYCOSYLATION; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; INFLAMMATION; LYSOSOME STORAGE DISEASE; MACROPHAGE; MASS SPECTROMETRY; MOUSE; NONHUMAN; PRIORITY JOURNAL;

1-DEOXYNOJIRIMYCIN; ANIMALS; APOPTOSIS; BETA-N-ACETYLHEXOSAMINIDASES; CELL LINE; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; ENZYME ACTIVATION; GANGLIOSIDOSES; GLYCOSPHINGOLIPIDS; IMINO SUGARS; KINETICS; LYSOSOMES; MASS SPECTROMETRY; MICE; OLIGOSACCHARIDES;

MURINAE;

EID: 77952027497     PISSN: 02820080     EISSN: 15734986     Source Type: Journal    
DOI: 10.1007/s10719-010-9278-1     Document Type: Article

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