The autoimmune lymphoproliferative syndrome: A rare disorder providing clues about normal tolerance

Autoimmunity Reviews

Volumn 9, Issue 7, 2010, Pages 488-493

  Turbyville, Joseph C ^a   Rao, V Koneti ^b  

^a WALTER REED ARMY MEDICAL CENTER   (United States)

^b NATIONAL INSTITUTE OF ALLERGY AND INFECTIOUS DISEASES   (United States)

Author keywords

ALPS; Autoimmune cytopenia; Double negative T cells; Endothelium; Fas

Indexed keywords

APOLIPOPROTEIN; AZATHIOPRINE; CORTICOSTEROID; CYCLOSPORIN; DEATH RECEPTOR 3; FAS ANTIGEN; HYDROXYCHLOROQUINE; IMMUNOGLOBULIN; MERCAPTOPURINE; METHOTREXATE; METHYLPREDNISOLONE; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; PREDNISONE; RAPAMYCIN; RITUXIMAB; TACROLIMUS; VINCRISTINE;

AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME; CELL PROLIFERATION; CLINICAL FEATURE; CYTOPENIA; DRUG DOSE REDUCTION; ENDOTHELIUM; GENE MUTATION; HEMOLYTIC ANEMIA; HEPATOMEGALY; HETEROZYGOSITY; HUMAN; INNATE IMMUNITY; LYMPHADENOPATHY; NEUTROPENIA; PATHOGENESIS; PHENOTYPE; POSITRON EMISSION TOMOGRAPHY; REVIEW; SPLENECTOMY; SPLENOMEGALY; TH2 CELL; THROMBOCYTOPENIA; ANIMAL; AUTOIMMUNITY; DIFFERENTIAL DIAGNOSIS; IMMUNOLOGICAL TOLERANCE; IMMUNOLOGY; INFLAMMATION; LYMPHATIC SYSTEM DISEASE; NATIONAL HEALTH ORGANIZATION; PATHOPHYSIOLOGY; RARE DISEASES; UNITED STATES;

ANIMALS; AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME; AUTOIMMUNITY; DIAGNOSIS, DIFFERENTIAL; ENDOTHELIUM; HUMANS; IMMUNE TOLERANCE; INFLAMMATION; LYMPHATIC DISEASES; NATIONAL INSTITUTES OF HEALTH (U.S.); RARE DISEASES; SPLENOMEGALY; UNITED STATES;

EID: 77951877292     PISSN: 15689972     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.autrev.2010.02.007     Document Type: Review

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