Myopathy-causing actin mutations promote defects in serum-response factor signalling

Biochemical Journal

Volumn 427, Issue 1, 2010, Pages 41-48

  Visegrády, Balázs ^a,b   Machesky, Laura M ^a  

^a BEATSON INSTITUTE FOR CANCER RESEARCH   (United Kingdom)

^b UNIVERSITY OF PÉCS   (Hungary)

Author keywords

Actin; Muscle; Myopathy; Nemaline myopathy; Serum response factor

Indexed keywords

ACTIN CYTOSKELETON; CULTURED CELL; IN-CELL; MUSCLE DEVELOPMENT; MUSCULAR DYSTROPHY; SERUM-RESPONSE FACTORS; SKELETAL MUSCLE; TRANSCRIPTIONAL RESPONSE;

BODY FLUIDS; CYTOLOGY; DEFECTS; GENE ENCODING; MUSCLE;

PROTEINS;

ALPHA SMOOTH MUSCLE ACTIN; F ACTIN; G ACTIN; SERUM RESPONSE FACTOR; ACTIN; LUCIFERASE;

ARTICLE; CONTROLLED STUDY; GENE MUTATION; HUMAN; HUMAN CELL; IN VITRO STUDY; MUSCLE DEVELOPMENT; MUSCLE GROWTH; MUTANT; NEMALINE MYOPATHY; PRIORITY JOURNAL; PROTEIN INTERACTION; SIGNAL TRANSDUCTION; TRANSCRIPTION REGULATION; CELL CULTURE; FLOW CYTOMETRY; FLUORESCENT ANTIBODY TECHNIQUE; GENETICS; IMMUNOPRECIPITATION; METABOLISM; MUTATION; SKELETAL MUSCLE; WESTERN BLOTTING;

ACTINS; BLOTTING, WESTERN; CELLS, CULTURED; FLOW CYTOMETRY; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; IMMUNOPRECIPITATION; LUCIFERASES; MUSCLE, SKELETAL; MUTATION; MYOPATHIES, NEMALINE; SERUM RESPONSE FACTOR; SIGNAL TRANSDUCTION;

EID: 77950887914     PISSN: 02646021     EISSN: 14708728     Source Type: Journal    
DOI: 10.1042/BJ20091641     Document Type: Article

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