α-Skeletal muscle actin nemaline myopathy mutants cause cell death in cultured muscle cells

Biochimica et Biophysica Acta - Molecular Cell Research

Volumn 1793, Issue 7, 2009, Pages 1259-1271

  Vandamme, Drieke ^a,b   Lambert, Ellen ^a,b   Waterschoot, Davy ^a,b   Cognard, Christian ^c   Vandekerckhove, Joël ^a,b   Ampe, Christophe ^a,b   Constantin, Bruno ^c   Rommelaere, Heidi ^a,b  

^a GHENT UNIVERSITY   (Belgium)

^b DEPARTMENT OF PLANT SYSTEMS BIOLOGY   (Belgium)

^c UNIVERSITÉ DE POITIERS   (France)

Author keywords

Actin; Cell death; Myoblast; Myotube; Nemaline myopathy

Indexed keywords

ALLOGRAFT INFLAMMATORY FACTOR 1; ALPHA ACTIN; CALPAIN; CASPASE; ENDONUCLEASE G; MUTANT PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; APOPTOSIS; ARTICLE; CELL AGGREGATION; CELL CULTURE; CELL DEATH; CELL DIFFERENTIATION; CONTROLLED STUDY; GENE MUTATION; MUSCLE CELL; MUSCLE HYPOTONIA; MUSCLE WEAKNESS; MYOBLAST; MYOFILAMENT; MYOTUBE; NEMALINE MYOPATHY; NEWBORN; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FOLDING; RAT;

ACTINS; ANIMALS; ANIMALS, NEWBORN; APOPTOSIS; APOPTOSIS INDUCING FACTOR; CALPAIN; CASPASES; CELL DIFFERENTIATION; CELL MEMBRANE; CELLS, CULTURED; ENDODEOXYRIBONUCLEASES; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; MUSCLE FIBERS, SKELETAL; MUSCLE, SKELETAL; MUTAGENESIS, SITE-DIRECTED; MUTATION; MYOBLASTS; MYOPATHIES, NEMALINE; PHENOTYPE; PROTEIN CONFORMATION; RATS;

EID: 67649394146     PISSN: 01674889     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbamcr.2009.04.004     Document Type: Article

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