Early onset of cardiomyopathy and primary prevention of sudden death in X-linked Emery-Dreifuss muscular dystrophy

Neuromuscular Disorders

Volumn 20, Issue 3, 2010, Pages 174-177

  Nigro, Gerardo ^a   Russo, Vincenzo ^a   Ventriglia, Vega Maria ^a   Cioppa, Nadia Della ^b   Palladino, Alberto ^a   Nigro, Vincenzo ^a   Calabrò, Raffaele ^a   Nigro, Giovanni ^a   Politano, Luisa ^a  

^a SECOND UNIVERSITY OF NAPLES   (Italy)

^b MONALDI HOSPITAL   (Italy)

Author keywords

Cardiomyopathy; Implantable cardioverter defibrillator; Novel mutation; Primary prevention; Sudden cardiac death; X linked Emery Dreifuss muscular dystrophy

Indexed keywords

CREATINE KINASE;

ADOLESCENT; ARTICLE; ATRIOVENTRICULAR BLOCK; CARDIOMYOPATHY; CASE REPORT; CHILD; CREATINE KINASE BLOOD LEVEL; DEFIBRILLATOR; DOPPLER ECHOCARDIOGRAPHY; ELECTROCARDIOGRAM; EMERY DREIFUSS MUSCULAR DYSTROPHY; FALLING; HOLTER MONITORING; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; IMPLANTATION; MALE; MUSCLE ATROPHY; MUSCLE BIOPSY; MUSCLE WEAKNESS; ONSET AGE; PRIMARY PREVENTION; PRIORITY JOURNAL; SICK SINUS SYNDROME; SUDDEN DEATH; SUPRAVENTRICULAR PREMATURE BEAT; SYNCOPE;

ADOLESCENT; CARDIOMYOPATHIES; DEATH, SUDDEN, CARDIAC; DEFIBRILLATORS, IMPLANTABLE; ELECTROCARDIOGRAPHY; HUMANS; MALE; MUSCULAR DYSTROPHY, EMERY-DREIFUSS; SICK SINUS SYNDROME; TACHYCARDIA, VENTRICULAR;

EID: 77950516221     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nmd.2009.12.004     Document Type: Article

References (10)

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