Guanidino compound levels in blood, cerebrospinal fluid, and post-mortem brain material of patients with argininemia

Molecular Genetics and Metabolism

Volumn 100, Issue SUPPL., 2010, Pages

  Deignan, Joshua L ^a   De Deyn, Peter P ^b   Cederbaum, Stephen D ^a   Fuchshuber, Arno ^c   Roth, Bernhard ^c   Gsell, Wieland ^d   Marescau, Bart ^b  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF ANTWERP   (Belgium)

^c UNIVERSITY OF COLOGNE   (Germany)

^d UNIVERSITY OF WÜRZBURG   (Germany)

Author keywords

Ammonia; Arginase; Arginase I deficiency; Arginine; Argininemia; Catabolites of arginine; Guanidino compounds; Guanidino group

Indexed keywords

5 GUANIDINO 2 OXOVALERIC ACID; AGMATINE; ALPHA N ACETYLARGININE; ARGININE; ARGININIC ACID; GUANIDINE DERIVATIVE; GUANIDINOACETIC ACID; HOMOARGININE; NITRIC OXIDE; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; AGED; ARTICLE; AUTOPSY; BLOOD LEVEL; CEREBROSPINAL FLUID LEVEL; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; HUMAN; HUMAN TISSUE; HYPERAMMONEMIA; PATHOPHYSIOLOGY; PRIORITY JOURNAL; SPASTICITY; SYMPTOMATOLOGY;

ADOLESCENT; ADULT; AUTOPSY; BRAIN; CHILD; CHILD, PRESCHOOL; FOLLOW-UP STUDIES; GUANIDINES; HUMANS; HYPERARGININEMIA; MALE; MULTIPLE ORGAN FAILURE; TIME FACTORS; UREA; YOUNG ADULT;

EID: 77950341453     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2010.01.012     Document Type: Article

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