Increased plasma and tissue guanidino compounds in a mouse model of hyperargininemia

Molecular Genetics and Metabolism

Volumn 93, Issue 2, 2008, Pages 172-178

  Deignan, Joshua L ^a   Marescau, Bart ^b   Livesay, Justin C ^a   Iyer, Ramaswamy K ^a   De Deyn, Peter P ^b   Cederbaum, Stephen D ^a   Grody, Wayne W ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF ANTWERP   (Belgium)

Author keywords

Ammonia; Arginase; Arginine; Guanidino compounds; Ornithine

Indexed keywords

5 GUANIDINO 2 OXOVALERIC ACID; ALPHA N ACETYLARGININE; AMMONIA; ARGINASE 1; ARGININE; ARGININIC ACID; GUANIDINE DERIVATIVE; NEUROTOXIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN; CEREBROSPINAL FLUID ANALYSIS; CLINICAL FEATURE; CONTROLLED STUDY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; GROWTH RETARDATION; HYPERAMMONEMIA; INTELLECTUAL IMPAIRMENT; KIDNEY; KNOCKOUT MOUSE; LIVER; MOUSE; NONHUMAN; PLASMA; PRIORITY JOURNAL; SPASTICITY; STATISTICAL ANALYSIS; UREMIA;

ANIMALS; ARGINASE; BLOOD-BRAIN BARRIER; BRAIN; DISEASE MODELS, ANIMAL; GUANIDINES; HUMANS; HYPERARGININEMIA; KIDNEY; LIVER; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT;

ANIMALIA; MAMMALIA;

EID: 38048999447     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2007.09.016     Document Type: Article

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