Glomerular and proximal tubule cysts as early manifestations of Pkd1 deletion

Nephrology Dialysis Transplantation

Volumn 25, Issue 4, 2010, Pages 1067-1078

  Ahrabi, Ali K ^a,e   Jouret, Franois ^a   Marbaix, Etienne ^a   Delporte, Christine ^b   Horie, Shigeo ^c   Mulroy, Sharon ^d   Boulter, Catherine ^d   Sandford, Richard ^d   Devuyst, Olivier ^a  

^a UNIVERSITÉ CATHOLIQUE DE LOUVAIN   (Belgium)

^b UNIVERSITÉ LIBRE DE BRUXELLES   (Belgium)

^c TEIKYO UNIVERSITY   (Japan)

^d UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^e BRIGHAM AND WOMEN S HOSPITAL   (United States)

Author keywords

Cystogenesis; Glomerular and proximal tubule cysts; Low molecular weight protein; Megalin; Polyhydramnios

Indexed keywords

AGGLUTININ; CYCLIC AMP; GLUCOSE; LECTIN; MEGALIN; POLYCYSTIN 1; SODIUM;

AMNION FLUID ANALYSIS; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CELL MATURATION; CONTROLLED STUDY; DISEASE ASSOCIATION; DOLICHOS; EMBRYO; EPITHELIUM CELL; GENE DELETION; GENE EXPRESSION REGULATION; GLOMERULAR CYST; GLUCOSURIA; HYDRAMNIOS; KIDNEY COLLECTING TUBULE; KIDNEY DISEASE; KIDNEY PROXIMAL TUBULE CYST; LETHALITY; MESENCHYME; MOUSE; NONHUMAN; PLACENTA DISORDER; PRIORITY JOURNAL; SODIUM EXCRETION; SOLUTE; URETER;

ANIMALS; BETA-GALACTOSIDASE; CYCLIC AMP; EMBRYO, MAMMALIAN; FEMALE; GENE DELETION; HOMOZYGOTE; IMMUNOENZYME TECHNIQUES; KIDNEY GLOMERULUS; KIDNEY TUBULES, PROXIMAL; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; PLACENTA; POLYCYSTIC KIDNEY DISEASES; POLYHYDRAMNIOS; PREGNANCY; SURVIVAL RATE; TRPP CATION CHANNELS;

EID: 77950256964     PISSN: 09310509     EISSN: 14602385     Source Type: Journal    
DOI: 10.1093/ndt/gfp611     Document Type: Article

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