Glycogen storage disease type 1: Impact of medium-chain triglycerides on metabolic control and growth

Annals of Nutrition and Metabolism

Volumn 56, Issue 3, 2010, Pages 225-232

  Das, Anibh M ^a   Lücke, Thomas ^a   Meyer, Uta ^a   Hartmann, Hans ^a   Illsinger, Sabine ^a  

^a HANNOVER MEDICAL SCHOOL   (Germany)

Author keywords

Carnitine palmitoyltransferase; Fatty acid oxidation; Glycogen storage disease type 1; Growth; Medium chain triglycerides; Triglycerides

Indexed keywords

CARNITINE PALMITOYLTRANSFERASE I; GLUCOSE; KETONE BODY; LACTIC ACID; MALONYL COENZYME A; MEDIUM CHAIN TRIACYLGLYCEROL; URIC ACID;

ADULT; ARTICLE; CASE REPORT; CHILD; DIET THERAPY; ENZYME SYNTHESIS; FATTY ACID OXIDATION; FEMALE; GLUCOSE BLOOD LEVEL; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; HYPERTRIGLYCERIDEMIA; HYPOGLYCEMIA; LACTATE BLOOD LEVEL; MALE; METABOLIC REGULATION; NUTRITIONAL SUPPORT; PRIORITY JOURNAL; TREATMENT OUTCOME; URIC ACID BLOOD LEVEL;

ADULT; BODY HEIGHT; BODY WEIGHT; CHILD, PRESCHOOL; DIET; DIETARY CARBOHYDRATES; DIETARY FATS; ENERGY INTAKE; ENERGY METABOLISM; FEMALE; GLYCOGEN STORAGE DISEASE TYPE I; GROWTH; HUMANS; INFANT; KETONE BODIES; LACTATES; TASTE; TRIGLYCERIDES; URIC ACID;

EID: 77950063750     PISSN: 02506807     EISSN: None     Source Type: Journal    
DOI: 10.1159/000283242     Document Type: Article

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