Improvements of hypertriglyceridemia and hyperlacticemia in Japanese children with glycogen storage disease type Ia by medium-chain triglyceride milk

European Journal of Pediatrics

Volumn 166, Issue 10, 2007, Pages 1009-1016

  Nagasaka, Hironori ^a   Hirano, Ken Ichi ^b   Ohtake, Akira ^c   Miida, Takashi ^d   Takatani, Tomozumi ^e   Murayama, Kei ^a   Yorifuji, Tohru ^f   Kobayashi, Kunihiko ^g   Kanazawa, Masaki ^e   Ogawa, Atsushi ^e   Takayanagi, Masaki ^a  

^a CHIBA CHILDREN'S HOSPITAL   (Japan)

^b OSAKA UNIVERSITY   (Japan)

^c SAITAMA MEDICAL UNIVERSITY   (Japan)

^d NIIGATA UNIVERSITY GRADUATE SCHOOL OF MEDICAL AND DENTAL SCIENCES   (Japan)

^e CHIBA UNIVERSITY   (Japan)

^f KYOTO UNIVERSITY   (Japan)

^g HOKKAIDO UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Fatty acid beta oxidation; Glycogen storage disease type Ia; Hyperlacticemia; Hypertriglyceridemia; Hypoglycemia; Medium chain triglyceride milk

Indexed keywords

ACYLCARNITINE; BEZAFIBRATE; CARNITINE; GLUCOSE; HIGH DENSITY LIPOPROTEIN CHOLESTEROL; KETONE BODY; MEDIUM CHAIN TRIACYLGLYCEROL; STARCH;

ADOLESCENT; ANAMNESIS; ARTICLE; CARBOHYDRATE METABOLISM; CASE REPORT; CHILD; CHILD HEALTH; CHOLESTEROL BLOOD LEVEL; CLINICAL FEATURE; CONTROLLED STUDY; CREATININE BLOOD LEVEL; DRUG MECHANISM; G727T GENE; GENE MUTATION; GENETIC ANALYSIS; GLUCOSE BLOOD LEVEL; GLYCOGEN STORAGE DISEASE TYPE 1; GLYCOGEN STORAGE DISEASE TYPE 1A; HOSPITAL ADMISSION; HUMAN; HUMAN TISSUE; HYPERLACTATEMIA; HYPERTRIGLYCERIDEMIA; HYPOGLYCEMIA; INFANT; JAPANESE; LABORATORY TEST; LACTATE BLOOD LEVEL; LIPID METABOLISM; LIVER BIOPSY; LOW FAT DIET; MALE; MILK; MUTATOR GENE; PHYSICAL EXAMINATION; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; TREATMENT OUTCOME; TRIACYLGLYCEROL BLOOD LEVEL;

ADOLESCENT; ANIMALS; BIOLOGICAL MARKERS; CHILD, PRESCHOOL; CHOLESTEROL; DIETARY CARBOHYDRATES; DIETARY SUPPLEMENTS; GLYCOGEN STORAGE DISEASE TYPE I; GROWTH; HUMANS; HYPERTRIGLYCERIDEMIA; JAPAN; LACTATES; LACTIC ACID; LIPOPROTEINS; MALE; MILK; TRIGLYCERIDES;

EID: 34548146024     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-006-0372-0     Document Type: Article

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