-
1
-
-
0026523829
-
Cystic fibrosis: Molecular biology and therapeutic implications
-
Collins FS. Cystic fibrosis: Molecular biology and therapeutic implications. Science 1992 256 : 774 779.
-
(1992)
Science
, vol.256
, pp. 774-779
-
-
Collins, F.S.1
-
2
-
-
52649120753
-
RNA interference for CFTR attenuates lung fluid absorption at birth in rats
-
Li T, Koshy S, Folkesson HG. RNA interference for CFTR attenuates lung fluid absorption at birth in rats. Respir. Res. 2008 9 : 55.
-
(2008)
Respir. Res.
, vol.9
, pp. 55
-
-
Li, T.1
Koshy, S.2
Folkesson, H.G.3
-
4
-
-
21644465164
-
Normal CFTR activity and reversed skin potentials in pseudohypoaldosteronism
-
Reddy MM, Wang XF, Gottschalk M, Jones K, Quinton PM. Normal CFTR activity and reversed skin potentials in pseudohypoaldosteronism. J. Membr. Biol. 2005 203 : 151 159.
-
(2005)
J. Membr. Biol.
, vol.203
, pp. 151-159
-
-
Reddy, M.M.1
Wang, X.F.2
Gottschalk, M.3
Jones, K.4
Quinton, P.M.5
-
5
-
-
4344707707
-
Severe osteopenia in CFTR-null mice
-
Dif F, Marty C, Baudoin C, de Vernejoul MC, Levi G. Severe osteopenia in CFTR-null mice. Bone 2004 35 : 595 603.
-
(2004)
Bone
, vol.35
, pp. 595-603
-
-
Dif, F.1
Marty, C.2
Baudoin, C.3
De Vernejoul, M.C.4
Levi, G.5
-
6
-
-
38849119609
-
Persistent osteopenia in adult cystic fibrosis transmembrane conductance regulator-deficient mice
-
Haston CK, Li W, Li A, Lafleur M, Henderson JE. Persistent osteopenia in adult cystic fibrosis transmembrane conductance regulator-deficient mice. Am. J. Respir. Crit. Care Med. 2008 177 : 309 315.
-
(2008)
Am. J. Respir. Crit. Care Med.
, vol.177
, pp. 309-315
-
-
Haston, C.K.1
Li, W.2
Li, A.3
Lafleur, M.4
Henderson, J.E.5
-
7
-
-
61949178361
-
Murine model for cystic fibrosis bone disease demonstrates osteopenia and sex-related differences in bone formation
-
Pashuck TD, Franz SE, Altman MK et al. Murine model for cystic fibrosis bone disease demonstrates osteopenia and sex-related differences in bone formation. Pediatr. Res. 2009 65 : 311 316.
-
(2009)
Pediatr. Res.
, vol.65
, pp. 311-316
-
-
Pashuck, T.D.1
Franz, S.E.2
Altman, M.K.3
-
8
-
-
13444252961
-
Cystic fibrosis and bone disease: Are we missing a genetic link?
-
Aris RM, Guise TA. Cystic fibrosis and bone disease: Are we missing a genetic link? Eur. Respir. J. 2005 25 : 9 11.
-
(2005)
Eur. Respir. J.
, vol.25
, pp. 9-11
-
-
Aris, R.M.1
Guise, T.A.2
-
9
-
-
13444305413
-
Reduced bone density in cystic fibrosis: DeltaF508 mutation is an independent risk factor
-
King SJ, Topliss DJ, Kotsimbos T et al. Reduced bone density in cystic fibrosis: DeltaF508 mutation is an independent risk factor. Eur. Respir. J. 2005 25 : 54 61.
-
(2005)
Eur. Respir. J.
, vol.25
, pp. 54-61
-
-
King, S.J.1
Topliss, D.J.2
Kotsimbos, T.3
-
10
-
-
26944453604
-
Protocol for prevention and treatment of osteoporosis in patients with cystic fibrosis
-
Giron RM, Sanchez Molini P, Garcia Vadillo A et al. Protocol for prevention and treatment of osteoporosis in patients with cystic fibrosis. Med. Clin. 2005 125 : 325 328.
-
(2005)
Med. Clin.
, vol.125
, pp. 325-328
-
-
Giron, R.M.1
Sanchez Molini, P.2
Garcia Vadillo, A.3
-
11
-
-
3142684547
-
A study of bone mineral density in adult patients with cystic fibrosis
-
Giron RM, Sanchez Molini P, Almonacid C et al. A study of bone mineral density in adult patients with cystic fibrosis. Med. Clin. 2004 123 : 81 4.
-
(2004)
Med. Clin.
, vol.123
, pp. 81-4
-
-
Giron, R.M.1
Sanchez Molini, P.2
Almonacid, C.3
-
12
-
-
0036228542
-
Bone mineral density and quantitative ultrasound in adults with cystic fibrosis
-
Flohr F, Lutz A, App EM, Matthys H, Reincke M. Bone mineral density and quantitative ultrasound in adults with cystic fibrosis. Eur. J. Endocrinol. 2002 146 : 531 536.
-
(2002)
Eur. J. Endocrinol.
, vol.146
, pp. 531-536
-
-
Flohr, F.1
Lutz, A.2
App, E.M.3
Matthys, H.4
Reincke, M.5
-
13
-
-
0242488065
-
Osteoporosis is cystic fibrosis
-
Conway S. Osteoporosis is cystic fibrosis. J. Cyst. Fibros. 2003 2 : 161 162.
-
(2003)
J. Cyst. Fibros.
, vol.2
, pp. 161-162
-
-
Conway, S.1
-
14
-
-
0032721451
-
Low bone mineral density in adults with cystic fibrosis
-
Haworth CS, Selby PL, Webb AK et al. Low bone mineral density in adults with cystic fibrosis. Thorax 1999 54 : 961 967.
-
(1999)
Thorax
, vol.54
, pp. 961-967
-
-
Haworth, C.S.1
Selby, P.L.2
Webb, A.K.3
-
15
-
-
13444256205
-
Molecular mechanisms of endochondral bone development
-
Provot S, Schipani E. Molecular mechanisms of endochondral bone development. Biochem. Biophys. Res. Commun. 2005 328 : 658 665.
-
(2005)
Biochem. Biophys. Res. Commun.
, vol.328
, pp. 658-665
-
-
Provot, S.1
Schipani, E.2
-
17
-
-
0036197206
-
The life cycle of chondrocytes in the developing skeleton
-
Shum L, Nuckolls G. The life cycle of chondrocytes in the developing skeleton. Arthritis Res. 2002 4 : 94 106.
-
(2002)
Arthritis Res.
, vol.4
, pp. 94-106
-
-
Shum, L.1
Nuckolls, G.2
-
18
-
-
1642545091
-
Essential role of hypertrophic chondrocytes in endochondral bone development
-
Chung UI. Essential role of hypertrophic chondrocytes in endochondral bone development. Endocr. J. 2004 51 : 19 24.
-
(2004)
Endocr. J.
, vol.51
, pp. 19-24
-
-
Chung, U.I.1
-
19
-
-
14044269575
-
Immature murine articular chondrocytes in primary culture: A new tool for investigating cartilage
-
Salvat C, Pigenet A, Humbert L, Berenbaum F, Thirion S. Immature murine articular chondrocytes in primary culture: A new tool for investigating cartilage. Osteoarthritis Cartilage 2005 13 : 243 249.
-
(2005)
Osteoarthritis Cartilage
, vol.13
, pp. 243-249
-
-
Salvat, C.1
Pigenet, A.2
Humbert, L.3
Berenbaum, F.4
Thirion, S.5
-
20
-
-
0036896008
-
Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion
-
Ma T, Thiagarajah JR, Yang H et al. Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion. J. Clin. Invest. 2002 110 : 1651 1658.
-
(2002)
J. Clin. Invest.
, vol.110
, pp. 1651-1658
-
-
Ma, T.1
Thiagarajah, J.R.2
Yang, H.3
-
21
-
-
0036203870
-
Volume increase in growth plate chondrocytes during hypertrophy: The contribution of organic osmolytes
-
Farnum CE, Lee R, O'Hara K, Urban JP. Volume increase in growth plate chondrocytes during hypertrophy: The contribution of organic osmolytes. Bone 2002 30 : 574 581.
-
(2002)
Bone
, vol.30
, pp. 574-581
-
-
Farnum, C.E.1
Lee, R.2
O'Hara, K.3
Urban, J.P.4
-
22
-
-
47249140827
-
Congenital tracheal malformation in cystic fibrosis transmembrane conductance regulator-deficient mice
-
Bonvin E, Le Rouzic P, Bernaudin JF et al. Congenital tracheal malformation in cystic fibrosis transmembrane conductance regulator-deficient mice. J. Physiol. 2008 586 : 3231 3243.
-
(2008)
J. Physiol.
, vol.586
, pp. 3231-3243
-
-
Bonvin, E.1
Le Rouzic, P.2
Bernaudin, J.F.3
|