Murine hippocampal neurons expressing Fmr1 gene premutations show early developmental deficits and late degeneration

Human Molecular Genetics

Volumn 19, Issue 1, 2009, Pages 196-208

  Chen, Yucui ^a   Tassone, Flora ^a,b   Berman, Robert F ^a,b   Hagerman, Paul J ^a,b   Hagerman, Randi J ^a,b   Willemsen, Rob ^c   Pessah, Isaac N ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c ERASMUS MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

FRAGILE X MENTAL RETARDATION PROTEIN; MESSENGER RNA; PHALLOIDIN; SYNAPSIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BRAIN NERVE CELL; CONTROLLED STUDY; DEGENERATIVE DISEASE; DENDRITIC CELL; DEVELOPMENTAL DISORDER; FEMALE; FRAGILE X ASSOCIATED TREMOR ATAXIA SYNDROME; HETEROZYGOTE; HIPPOCAMPUS; IMMUNOFLUORESCENCE TEST; IN VITRO STUDY; MORPHOMETRICS; MOUSE; NERVE GROWTH; NEUROPATHOLOGY; NEWBORN; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; SYNAPTIC TRANSMISSION; TRINUCLEOTIDE REPEAT; WILD TYPE; ANIMAL; CELL SURVIVAL; CONGENITAL MALFORMATION; DENDRITE; GENETICS; HETEROCHROMATIN; METABOLISM; NERVE CELL; NERVE DEGENERATION; PATHOLOGY; SYNAPTOSOME; TIME;

MURINAE; MUS;

ANIMALS; CELL SURVIVAL; DENDRITES; FRAGILE X MENTAL RETARDATION PROTEIN; HETEROCHROMATIN; HETEROZYGOTE; HIPPOCAMPUS; MICE; NERVE DEGENERATION; NEURONS; PHALLOIDINE; PRESYNAPTIC TERMINALS; RNA, MESSENGER; SYNAPSINS; TIME FACTORS; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 77649301567     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddp479     Document Type: Article

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