Ectopic expression of CGG containing mRNA is neurotoxic in mammals

Human Molecular Genetics

Volumn 18, Issue 13, 2009, Pages 2443-2451

  Hashem, Vera ^a   Galloway, Jocelyn N ^a   Mori, Mayra ^a   Willemsen, Rob ^b   Oostra, Ben A ^b   Paylor, Richard ^a   Nelson, David L ^a  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b ERASMUS MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

CYTIDINE; FRAGILE X MENTAL RETARDATION PROTEIN; GREEN FLUORESCENT PROTEIN; GUANIDINE; MESSENGER RNA;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL LOSS; CELL SWELLING; CEREBELLUM; CONTROLLED STUDY; DEGENERATIVE DISEASE; DISEASE ASSOCIATION; DISEASE MODEL; FRAGILE X ASSOCIATED TREMOR ATAXIA SYNDROME; FRAGILE X SYNDROME; GENE CONSTRUCT; GENE EXPRESSION; GENE FUNCTION; GENE MUTATION; GENOTYPE; MOTOR COORDINATION; NERVE CELL NECROSIS; NERVE DEGENERATION; NONHUMAN; ONSET AGE; PRIORITY JOURNAL; PURKINJE CELL; TRANSGENE; TRINUCLEOTIDE REPEAT;

AGE FACTORS; ANIMALS; CELL DEATH; DISEASE MODELS, ANIMAL; FRAGILE X MENTAL RETARDATION PROTEIN; FRAGILE X SYNDROME; GENE EXPRESSION; HUMANS; INTRANUCLEAR INCLUSION BODIES; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; NEURONS; RNA, MESSENGER; TRINUCLEOTIDE REPEAT EXPANSION;

MAMMALIA; MUS;

EID: 67249150481     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddp182     Document Type: Article

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