Long-chain polyunsaturated fatty acid status in phenylketonuric patients treated with tetrahydrobiopterin

Clinical Biochemistry

Volumn 43, Issue 4-5, 2010, Pages 411-415

  Vilaseca, Maria A ^a,c   Lambruschini, Nilo ^b,c   Gómez López, Lilianne ^b,c,d   Gutiérrez, Alejandra ^b,c   Moreno, Juan ^a   Tondo, Mireia ^a   Artuch, Rafael ^a,c,d   Campistol, Jaume ^a,c,d  

^a Department of Biochemistry ^*  (Spain)

^b Division of Pediatric Gastroenterology Hepatology and Nutrition   (Spain)

^c UNIVERSITY OF BARCELONA   (Spain)

^d INSTITUTO DE SALUD CARLOS III   (Spain)

Author keywords

Arachidonic acid; BH4 therapy; Docosahexaenoic acid; Essential fatty acids; Long chain polyunsaturated fatty acid; Mild hyperphenylalaninemia; n 3 PUFA; n 6 PUFA; Phenylketonuria; Tetrahydrobiopterin

Indexed keywords

ARACHIDONIC ACID; CARNITINE; CHOLESTEROL; DOCOSAHEXAENOIC ACID; ESSENTIAL FATTY ACID; LONG CHAIN FATTY ACID; OMEGA 3 FATTY ACID; OMEGA 6 FATTY ACID; PHENYLALANINE; POLYUNSATURATED FATTY ACID; TETRAHYDROBIOPTERIN;

ADOLESCENT; ARTICLE; CHILD; CHOLESTEROL BLOOD LEVEL; CONTROLLED STUDY; CROSS-SECTIONAL STUDY; DRUG RESPONSE; ERYTHROCYTE LEVEL; FATTY ACID ANALYSIS; FATTY ACID BLOOD LEVEL; GAS CHROMATOGRAPHY; HUMAN; HYPERPHENYLALANINEMIA; INTERMETHOD COMPARISON; LIPID COMPOSITION; MAJOR CLINICAL STUDY; NUTRITIONAL STATUS; NUTRITIONAL TOLERANCE; PHENYLKETONURIA; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN RESTRICTION; REFERENCE VALUE; SCHOOL CHILD; TREATMENT DURATION;

ADOLESCENT; BIOPTERIN; CHILD; CHILD, PRESCHOOL; DIET; DOCOSAHEXAENOIC ACIDS; ERYTHROCYTES; FATTY ACIDS, UNSATURATED; HUMANS; INFANT; PHENYLKETONURIAS; PHOSPHOLIPIDS; REFERENCE VALUES;

EID: 76749161846     PISSN: 00099120     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.clinbiochem.2009.11.013     Document Type: Article

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