A G-protein editor gates coenzyme B12 loading and is corrupted in methylmalonic aciduria

Proceedings of the National Academy of Sciences of the United States of America

Volumn 106, Issue 51, 2009, Pages 21567-21572

  Padovani, Dominique ^a   Banerjee, Ruma ^a  

^a UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

Author keywords

Cobalamin; Trafficking

Indexed keywords

ADENOSYLTRANSFERASE; CHAPERONE; COBAMAMIDE; GUANINE NUCLEOTIDE BINDING PROTEIN; METHYLMALONYL COENZYME A MUTASE; PROTEIN MEAB; TRANSFERASE; UNCLASSIFIED DRUG;

ARTICLE; CATALYSIS; ENZYME ACTIVITY; ENZYME KINETICS; GENE MUTATION; HUMAN; HUMAN CELL; METHYLMALONIC ACIDURIA; OXIDATION; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN FUNCTION; THERMODYNAMICS;

BASE SEQUENCE; CALORIMETRY; COBAMIDES; DNA PRIMERS; ELECTRON SPIN RESONANCE SPECTROSCOPY; GTP-BINDING PROTEINS; GUANOSINE TRIPHOSPHATE; HUMANS; KINETICS; METABOLISM, INBORN ERRORS; METHYLMALONIC ACID; METHYLMALONYL-COA MUTASE; MODELS, MOLECULAR; MUTATION; THERMODYNAMICS;

EID: 76049120274     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.0908106106     Document Type: Article

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