GAP43 overexpression and enhanced neurite outgrowth in mucopolysaccharidosis type IIIB cortical neuron cultures

Journal of Neuroscience Research

Volumn 88, Issue 1, 2010, Pages 202-213

  Hocquemiller, Michaël ^a   Vitry, Sandrine ^a   Bigou, Stéphanie ^b   Bruyère, Julie ^a   Ausseil, Jérôme ^a   Heard, Jean Michel ^a  

^a INSTITUT PASTEUR   (France)

^b BICÊTRE HOSPITAL   (France)

Author keywords

Cortical neuron culture; Lysosomal storage disease; Neuritogenesis; Oligosaccharides; Sanfilippo syndrome

Indexed keywords

HEPARAN SULFATE; LYSOSOME ENZYME; MESSENGER RNA; NEUROMODULIN; OLIGOSACCHARIDE; PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BRAIN CELL; CELL CULTURE; CELL ELONGATION; CELL FUNCTION; CONTROLLED STUDY; DENDRITE; DYNAMICS; EMBRYO; FEMALE; GENE EXPRESSION; GENE OVEREXPRESSION; GENETIC DISORDER; MALE; MOUSE; MOUSE EMBRYO; NERVE CELL DIFFERENTIATION; NERVE FIBER; NERVE FIBER GROWTH; NEURITE; NONHUMAN; OBSERVATION; PHENOTYPE; POPULATION; PRIORITY JOURNAL; SANFILIPPO SYNDROME;

ANIMALS; BLOTTING, WESTERN; CELL SHAPE; CELLS, CULTURED; CEREBRAL CORTEX; DISEASE MODELS, ANIMAL; FLUORESCENT ANTIBODY TECHNIQUE; GAP-43 PROTEIN; GENE EXPRESSION; GENETIC VECTORS; LENTIVIRUS; MICE; MUCOPOLYSACCHARIDOSIS III; NEURITES; NEURONAL PLASTICITY; NEURONS; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; STATISTICS, NONPARAMETRIC; TIME FACTORS;

EID: 73949149946     PISSN: 03604012     EISSN: 10974547     Source Type: Journal    
DOI: 10.1002/jnr.22190     Document Type: Article

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