Cardiomyopathies in Propionic Aciduria are Reversible After Liver Transplantation

Journal of Pediatrics

Volumn 156, Issue 1, 2010, Pages 128-134

  Romano, Stéphane ^a   Valayannopoulos, Vassili ^a,b   Touati, Guy ^a   Jais, Jean Pierre ^a   Rabier, Daniel ^a   de Keyzer, Yves ^b   Bonnet, Damien ^a   de Lonlay, Pascale ^a,b  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

^b INSERM   (France)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID MIXTURE; ANTIBIOTIC AGENT; CARNITINE; PROPIONIC ACID;

ACIDURIA; ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CLINICAL EVALUATION; CLINICAL FEATURE; COMPARATIVE STUDY; CONGESTIVE CARDIOMYOPATHY; DISEASE ASSOCIATION; DISEASE COURSE; FEMALE; GROUPS BY AGE; HEART ARREST; HUMAN; INBORN ERROR OF METABOLISM; LIVER TRANSPLANTATION; MALE; METABOLITE; MORTALITY; NEWBORN PERIOD; PRESCHOOL CHILD; PRIORITY JOURNAL; PROPIONIC ACIDURIA; PROTEIN RESTRICTION; RETROSPECTIVE STUDY; SCHOOL CHILD; SURVIVAL; TREATMENT CONTRAINDICATION; URINARY EXCRETION;

CARDIOMYOPATHY, DILATED; CARNITINE; CHILD; CHILD, PRESCHOOL; HUMANS; LIVER TRANSPLANTATION; PROPIONATES; PROPIONIC ACIDEMIA; RETROSPECTIVE STUDIES; VITAMIN B COMPLEX;

EID: 72049099057     PISSN: 00223476     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jpeds.2009.07.002     Document Type: Article

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