Dominant pro-vasopressin mutants that cause diabetes insipidus form disulfide-linked fibrillar aggregates in the endoplasmic reticulum

Journal of Cell Science

Volumn 122, Issue 21, 2009, Pages 3994-4002

  Birk, Julia ^a   Friberg, Michael A ^a   Prescianotto Baschong, Christina ^a   Spiess, Martin ^a   Rutishauser, Jonas ^a  

^a UNIVERSITY OF BASEL   (Switzerland)

Author keywords

Aggregates; Diabetes insipidus; Fibrils; Neurophysin; Vasopressin

Indexed keywords

CALRETICULIN; CYSTEINE; FIBRIN; VASOPRESSIN;

ANIMAL CELL; ARTICLE; CONTROLLED STUDY; DIABETES INSIPIDUS; ENDOPLASMIC RETICULUM; FIBROBLAST; IMMUNOFLUORESCENCE; IMMUNOGOLD ELECTRON MICROSCOPY; MUTANT; NERVE CELL; NONHUMAN; OLIGOMERIZATION; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN LOCALIZATION;

ANIMALS; CERCOPITHECUS AETHIOPS; COS CELLS; DIABETES INSIPIDUS, NEUROGENIC; DISULFIDES; ENDOPLASMIC RETICULUM; HUMANS; MUTATION; PROTEIN CONFORMATION; PROTEIN FOLDING; PROTEIN PRECURSORS; VASOPRESSINS;

EID: 70450230337     PISSN: 00219533     EISSN: None     Source Type: Journal    
DOI: 10.1242/jcs.051136     Document Type: Article

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