Hemochromatosis: As a conformational disorder

International Journal of Biochemistry and Cell Biology

Volumn 41, Issue 11, 2009, Pages 2094-2097

  Gray, Steven G ^b   Crowe, John ^a   Lawless, Matthew W ^a  

^a MATER MISERICORDIAE UNIVERSITY HOSPITAL   (Ireland)

^b TRINITY COLLEGE DUBLIN   (Ireland)

Author keywords

Conformational disease; Endoplasmic reticulum stress; Hemochromatosis; Iron

Indexed keywords

4 PHENYLBUTYRIC ACID; BETA 2 MICROGLOBULIN; CYSTEINE; HEMOJUVELIN; HEPCIDIN; HFE PROTEIN; TAUROURSODEOXYCHOLIC ACID; TRANSFERRIN RECEPTOR 2; TYROSINE;

AMINO ACID SUBSTITUTION; CALCIUM HOMEOSTASIS; CELL SURFACE; CONFORMATIONAL TRANSITION; ENDOPLASMIC RETICULUM STRESS; HEMOCHROMATOSIS; HOMOZYGOSITY; HUMAN; INSULIN RESISTANCE; IRON METABOLISM; IRON OVERLOAD; NON INSULIN DEPENDENT DIABETES MELLITUS; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN FOLDING; PROTEIN LOCALIZATION; SHORT SURVEY; SIGNAL TRANSDUCTION;

ANIMALS; ENDOPLASMIC RETICULUM; HEMOCHROMATOSIS; HISTOCOMPATIBILITY ANTIGENS CLASS I; HUMANS; MEMBRANE PROTEINS; PROTEIN CONFORMATION;

EID: 70349432268     PISSN: 13572725     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.biocel.2009.04.006     Document Type: Short Survey

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