Neurological manifestations of acute intermittent porphyria

Cellular and Molecular Biology

Volumn 55, Issue 1, 2009, Pages 72-83

  Pischik, Elena ^a,b,c,d   Kauppinen, R ^a  

^a HELSINKI UNIVERSITY CENTRAL HOSPITAL   (Finland)

^b PAVLOV FIRST SAINT PETERSBURG STATE MEDICAL UNIVERSITY   (Russian Federation)

^c Clinical Diagnostic Centre with Policlinic in StPetersburg   (Russian Federation)

^d BIOMEDICUM HELSINKI   (Finland)

Author keywords

Acute intermittent poprhyria; Encephalopathy; MRI; Neuropathy; Porphyria; PRES

Indexed keywords

AMINOLEVULINIC ACID; PORPHOBILINOGEN DEAMINASE;

ABDOMINAL PAIN; ACHILLES REFLEX; ACUTE BRAIN DISEASE; ACUTE INTERMITTENT PORPHYRIA; AUTONOMIC DYSFUNCTION; AUTONOMIC NEUROPATHY; CENTRAL NERVOUS SYSTEM DISEASE; CLINICAL FEATURE; DISEASE SEVERITY; DYSAUTONOMIA; HEME SYNTHESIS; HUMAN; HYPOREFLEXIA; INAPPROPRIATE VASOPRESSIN SECRETION; LIVER DISEASE; MENTAL DISEASE; MYALGIA; NERVE CELL LESION; NEUROPATHIC PAIN; NEUROPATHOLOGY; NEUROPATHY; NEUROPHYSIOLOGY; NEUROTOXICITY; NUCLEAR MAGNETIC RESONANCE IMAGING; PATHOGENESIS; PERIPHERAL NEUROPATHY; POSTERIOR REVERSIBLE ENCEPHALOPATHY SYNDROME; PROGNOSIS; REVIEW; SEIZURE;

CENTRAL NERVOUS SYSTEM DISEASES; HUMANS; MAGNETIC RESONANCE IMAGING; NERVOUS SYSTEM DISEASES; NEUROPHYSIOLOGY; PERIPHERAL NERVOUS SYSTEM DISEASES; PORPHYRIA, ACUTE INTERMITTENT;

EID: 67449119677     PISSN: 01455680     EISSN: 1165158X     Source Type: Journal    
DOI: 10.1170/T841     Document Type: Review

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