-
2
-
-
23044442550
-
Scrapie, chronic wasting disease, and transmissible mink encephalopathy
-
Edited by Prusiner SB. New York, Woodbury
-
Prusiner SB, Williams E, Laplanche JL, Shinagawa M: Scrapie, chronic wasting disease, and transmissible mink encephalopathy. Prion Biology and Diseases. Edited by Prusiner SB. New York, Woodbury, 2004, pp 545-594
-
(2004)
Prion Biology and Diseases
, pp. 545-594
-
-
Prusiner, S.B.1
Williams, E.2
Laplanche, J.L.3
Shinagawa, M.4
-
3
-
-
0035928432
-
Tissue distribution of protease resistant prion protein in variant Creutzfeldt-Jakob disease using a highly sensitive immunoblotting assay
-
DOI 10.1016/S0140-6736(01)05403-4
-
Wadsworth JD, Joiner S, Hill AF, Campbell TA, Desbruslais M, Luthert PJ, Collinge J: Tissue distribution of protease resistant prion protein in variant Creutzfeldt-Jakob disease using a highly sensitive immunoblotting assay. Lancet 2001, 358:171-180 (Pubitemid 32718539)
-
(2001)
Lancet
, vol.358
, Issue.9277
, pp. 171-180
-
-
Wadsworth, J.D.F.1
Joiner, S.2
Hill, A.F.3
Campbell, T.A.4
Desbruslais, M.5
Luthert, P.J.6
Collinge, J.7
-
4
-
-
0242361687
-
Extraneural Pathologic Prion Protein in Sporadic Creutzfeldt-Jakob Disease
-
DOI 10.1056/NEJMoa030351
-
Glatzel M, Abela E, Maissen M, Aguzzi A: Extraneural pathologic prion protein in sporadic Creutzfeldt-Jakob disease. N Engl J Med 2003, 349:1812-1820 (Pubitemid 37362957)
-
(2003)
New England Journal of Medicine
, vol.349
, Issue.19
, pp. 1812-1820
-
-
Glatzel, M.1
Abela, E.2
Maissen, M.3
Aguzzi, A.4
-
5
-
-
0141849457
-
Acquired prion disease: Iatrogenic CJD, variant CJD, kuru
-
DOI 10.1093/bmb/66.1.255
-
Will RG: Acquired prion disease: iatrogenic CJD, variant CJD, kuru. Br Med Bull 2003, 66:255-265 (Pubitemid 37173506)
-
(2003)
British Medical Bulletin
, vol.66
, pp. 255-265
-
-
Will, R.G.1
-
6
-
-
78651041685
-
Degenerative disease of the central nervous system in New Guinea: The endemic occurrence of "kuru" in the native population
-
Gajdusek DC, Zigas V: Degenerative disease of the central nervous system in New Guinea: the endemic occurrence of "kuru" in the native population. N Engl J Med 1957, 257:974-978
-
(1957)
N Engl J Med
, vol.257
, pp. 974-978
-
-
Gajdusek, D.C.1
Zigas, V.2
-
7
-
-
0001149285
-
Changing patterns of kuru: Epidemiological changes in the period of increasing contact of the Fore people with western civilization
-
Alpers MP, Gajdusek DC: Changing patterns of kuru: epidemiological changes in the period of increasing contact of the Fore people with western civilization. Am J Trop Med Hyg 1965, 14:852-879
-
(1965)
Am J Trop Med Hyg
, vol.14
, pp. 852-879
-
-
Alpers, M.P.1
Gajdusek, D.C.2
-
8
-
-
33747040538
-
Iatrogenic Creutzfeldt-Jakob disease: The waning of an era
-
DOI 10.1212/01.wnl.0000231528.65069.3f, PII 0000611420060808000009
-
Brown P, Brandel JP, Preese M, Sato T: Iatrogenic Creutzfeldt-Jakob disease: the waning of an era. Neurology 2006, 67:389-393 (Pubitemid 44214958)
-
(2006)
Neurology
, vol.67
, Issue.3
, pp. 389-393
-
-
Brown, P.1
Brandel, J.-P.2
Preese, M.3
Sato, T.4
-
9
-
-
0342951746
-
A new variant of Creutzfeldt-Jakob disease in the UK
-
DOI 10.1016/S0140-6736(96)91412-9
-
Will RG, Ironside JW, Zeidler M, Cousens SN, Estibeiro K, Alperovitch A, Poser S, Pocchiari M, Hofman A, Smith PG: A new variant of Creutzfeldt-Jakob disease in the UK. Lancet 1996, 347:921-925 (Pubitemid 26102546)
-
(1996)
Lancet
, vol.347
, Issue.9006
, pp. 921-925
-
-
Will, R.G.1
Ironside, J.W.2
Zeidler, M.3
Cousens, S.N.4
Estibeiro, K.5
Alperovitch, A.6
Poser, S.7
Pocchiari, M.8
Hofmar, A.9
Smith, P.G.10
-
11
-
-
0028351904
-
Fatal familial insomnia and familial Creutzfeldt-Jakob disease: Different prion proteins determined by a DNA polymorphism
-
Monari L, Chen SG, Brown P, Parchi P, Petersen RB, Mikol J, Gray F, Cortelli P, Montagna P, Ghetti B, Goldfarb LG, Gajdusek DC, Lugaresi E, Gambetti P, Autilio-Gambetti L: Fatal familial insomnia and familial Creutzfeldt-Jakob disease: different prion proteins determined by a DNA polymorphism. Proc Natl Acad Sci USA 1994, 91:2839-2842 (Pubitemid 24139444)
-
(1994)
Proceedings of the National Academy of Sciences of the United States of America
, vol.91
, Issue.7
, pp. 2839-2842
-
-
Monari, L.1
Chen, S.G.2
Brown, P.3
Parchi, P.4
Petersen, R.B.5
Mikol, J.6
Gray, F.7
Cortelli, P.8
Montagna, P.9
Ghetti, B.10
Goldfarb, L.G.11
Gajdusek, D.C.12
Lugaresi, E.13
Gambetti, P.14
Autilio-Gambetti, L.15
-
12
-
-
0029027854
-
Truncated forms of the human prion protein in normal brain and in prion diseases
-
Chen SG, Teplow DB, Parchi P, Teller JK, Gambetti P, Autilio-Gambetti L: Truncated forms of the human prion protein in normal brain and in prion diseases. J Biol Chem 1995, 270:19173-19180
-
(1995)
J Biol Chem
, vol.270
, pp. 19173-19180
-
-
Chen, S.G.1
Teplow, D.B.2
Parchi, P.3
Teller, J.K.4
Gambetti, P.5
Autilio-Gambetti, L.6
-
13
-
-
0023499868
-
Mouse polyclonal and monoclonal antibody to scrapie-associated fibril proteins
-
Kascsak RJ, Rubenstein R, Merz PA, Tonna-DeMasi M, Fersko R, Carp RI, Wisniewski HM, Diringer H: Mouse polyclonal and monoclonal antibody to scrapie-associated fibril proteins. J Virol 1987, 61:3688-3693 (Pubitemid 18011463)
-
(1987)
Journal of Virology
, vol.61
, Issue.12
, pp. 3688-3693
-
-
Kascsak, R.J.1
Rubenstein, R.2
Merz, P.A.3
Tonna-DeMasi, M.4
Fersko, R.5
Carp, R.I.6
Wisniewski, H.M.7
Diringer, H.8
-
14
-
-
33845925066
-
Insoluble aggregates and protease-resistant conformers of prion protein in uninfected human brains
-
DOI 10.1074/jbc.M602238200
-
Yuan J, Xiao X, McGeehan J, Dong Z, Cali I, Fujioka H, Kong Q, Kneale G, Gambetti P, Zou WQ: Insoluble aggregates and protease-resistant conformers of prion protein in uninfected human brains. J Biol Chem 2006, 281:34848-34858 (Pubitemid 46036524)
-
(2006)
Journal of Biological Chemistry
, vol.281
, Issue.46
, pp. 34848-34858
-
-
Yuan, J.1
Xiao, X.2
McGeehan, J.3
Dong, Z.4
Cali, I.5
Fujioka, H.6
Kong, Q.7
Kneale, G.8
Gambetti, P.9
Zou, W.-Q.10
-
15
-
-
0034682883
-
Preferential binding of fd gene 5 protein to tetraplex nucleic acid structures
-
Oliver AW, Bogdarina I, Schroeder E, Taylor IA, Kneale GG: Preferential binding of fd gene 5 protein to tetraplex nucleic acid structures. J Mol Biol 2000, 301:575-584
-
(2000)
J Mol Biol
, vol.301
, pp. 575-584
-
-
Oliver, A.W.1
Bogdarina, I.2
Schroeder, E.3
Taylor, I.A.4
Kneale, G.G.5
-
16
-
-
0026496257
-
Fatal familial insomnia and familial Creutzfeldt-Jakob disease: Disease phenotype determined by a DNA polymorphism
-
Goldfarb LG, Petersen RB, Tabaton M, Brown P, LeBlanc AC, Montagna P, Cortelli P, Julien J, Vital C, Pendelbury WW, Haltia M, Willis PR, Hauw JJ, McKeever PE, Monari L, Schrank B, Swergold GD, Autilio-Gambetti L, Gajdusek C, Lugaresi E, Gambetti P: Fatal familial insomnia and familial Creutzfeldt-Jakob disease: disease phenotype determined by a DNA polymorphism. Science 1992, 258:806-808
-
(1992)
Science
, vol.258
, pp. 806-808
-
-
Goldfarb, L.G.1
Petersen, R.B.2
Tabaton, M.3
Brown, P.4
LeBlanc, A.C.5
Montagna, P.6
Cortelli, P.7
Julien, J.8
Vital, C.9
Pendelbury, W.W.10
Haltia, M.11
Willis, P.R.12
Hauw, J.J.13
McKeever, P.E.14
Monari, L.15
Schrank, B.16
Swergold, G.D.17
Autilio-Gambetti, L.18
Gajdusek, C.19
Lugaresi, E.20
Gambetti, P.21
more..
-
17
-
-
8944259890
-
Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease
-
DOI 10.1002/ana.410390613
-
Parchi P, Castellani R, Capellari S, Ghetti B, Young K, Chen SG, Farlow M, Dickson DW, Sima AA, Trojanowski JQ, Petersen RB, Gambetti P: Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Ann Neurol 1996, 39:767-778 (Pubitemid 26183813)
-
(1996)
Annals of Neurology
, vol.39
, Issue.6
, pp. 767-778
-
-
Parchi, P.1
Castellani, R.2
Capellari, S.3
Ghetti, B.4
Young, K.5
Chen, S.G.6
Farlow, M.7
Dickson, D.W.8
Sima, A.A.F.9
Trojanowski, J.Q.10
Petersen, R.B.11
Gambetti, P.12
-
18
-
-
28244491680
-
Creutzfeldt-Jakob disease (CJD) with a mutation at codon 148 of prion protein gene: Relationship with sporadic CJD
-
Pastore M, Chin SS, Bell KL, Dong Z, Yang Q, Yang L, Yuan J, Chen SG, Gambetti P, Zou WQ: Creutzfeldt-Jakob disease (CJD) with a mutation at codon 148 of prion protein gene: relationship with sporadic CJD. Am J Pathol 2005, 167:1729-1738 (Pubitemid 41713323)
-
(2005)
American Journal of Pathology
, vol.167
, Issue.6
, pp. 1729-1738
-
-
Pastore, M.1
Chin, S.S.2
Bell, K.L.3
Dong, Z.4
Yang, Q.5
Yang, L.6
Yuan, J.7
Chen, S.G.8
Gambetti, P.9
Zou, W.-Q.10
-
19
-
-
0037113898
-
Sc-like form
-
DOI 10.1074/jbc.M203611200
-
Zou WQ, Cashman NR: Acidic pH and detergents enhance in vitro conversion of human brain PrPC to a PrPSc-like form. J Biol Chem 2002, 277:43942-43947 (Pubitemid 36157818)
-
(2002)
Journal of Biological Chemistry
, vol.277
, Issue.46
, pp. 43942-43947
-
-
Zou, W.-Q.1
Cashman, N.R.2
-
20
-
-
0842277807
-
Antibody to DNA detects scrapie but not normal prion protein
-
DOI 10.1073/pnas.0307825100
-
Zou WQ, Zheng J, Gray DM, Gambetti P, Chen SG: Antibody to DNA detects scrapie but not normal prion protein. Proc Natl Acad Sci USA 2004, 101:1380-1385 (Pubitemid 38182697)
-
(2004)
Proceedings of the National Academy of Sciences of the United States of America
, vol.101
, Issue.5
, pp. 1380-1385
-
-
Zou, W.-Q.1
Zheng, J.2
Gray, D.M.3
Gambetti, P.4
Chen, S.G.5
-
21
-
-
46749121818
-
A novel human disease with abnormal prion protein sensitive to protease
-
Gambetti P, Dong Z, Yuan J, Xiao X, Zheng M, Alshekhlee A, Castellani R, Cohen M, Barria MA, Gonzalez-Romero D, Belay ED, Schonberger LB, Marder K, Harris C, Burke JR, Montine T, Wisniewski T, Dickson DW, Soto C, Hulette CM, Mastrianni JA, Kong Q, Zou WQ: A novel human disease with abnormal prion protein sensitive to protease. Ann Neurol 2008, 63:697-708
-
(2008)
Ann Neurol
, vol.63
, pp. 697-708
-
-
Gambetti, P.1
Dong, Z.2
Yuan, J.3
Xiao, X.4
Zheng, M.5
Alshekhlee, A.6
Castellani, R.7
Cohen, M.8
Barria, M.A.9
Gonzalez-Romero, D.10
Belay, E.D.11
Schonberger, L.B.12
Marder, K.13
Harris, C.14
Burke, J.R.15
Montine, T.16
Wisniewski, T.17
Dickson, D.W.18
Soto, C.19
Hulette, C.M.20
Mastrianni, J.A.21
Kong, Q.22
Zou, W.Q.23
more..
-
22
-
-
0035947588
-
PrP-C and PrP-Sc at the Fetal-Maternal Interface
-
DOI 10.1074/jbc.M008887200
-
Tuo W, Zhuang D, Knowles DP, Cheevers WP, Sy MS, O'Rourke KI: Prp-c and Prp-Sc at the fetal-maternal interface. J Biol Chem 2001, 276:18229-18234 (Pubitemid 37411393)
-
(2001)
Journal of Biological Chemistry
, vol.276
, Issue.21
, pp. 18229-18234
-
-
Tuo, W.1
Zhuang, D.2
Knowles, D.P.3
Cheevers, W.P.4
Sy, M.-S.5
O'Rourke, K.I.6
-
23
-
-
0035034926
-
Absence of protease-resistant prion protein in the cerebrospinal fluid of Creutzfeldt-Jakob disease
-
DOI 10.1002/path.872
-
Wong BS, Green AJ, Li R, Xie Z, Pan T, Liu T, Chen SG, Gambetti P, Sy MS: Absence of protease-resistant prion protein in the cerebrospinal fluid of Creutzfeldt-Jakob disease. J Pathol 2001, 194:9-14 (Pubitemid 32390442)
-
(2001)
Journal of Pathology
, vol.194
, Issue.1
, pp. 9-14
-
-
Gutierrez, P.S.1
Pires Jr., W.O.2
Marie, S.K.N.3
Moreira, L.F.P.4
Mady, C.5
Higuchi, M.L.6
Stolf, N.A.G.7
Ramires, J.A.F.8
-
24
-
-
18244383286
-
Sensitive detection of prion protein in human urine
-
Narang HK, Dagdanova A, Xie Z, Yang Q, Chen SG: Sensitive detection of prion protein in human urine. Exp Biol Med (Maywood) 2005, 230:343-349 (Pubitemid 40627686)
-
(2005)
Experimental Biology and Medicine
, vol.230
, Issue.5
, pp. 343-349
-
-
Narang, H.K.1
Dagdanova, A.2
Xie, Z.3
Yang, Q.4
Chen, S.G.5
-
25
-
-
58149378573
-
Prion diseases are efficiently transmitted by blood transfusion in sheep
-
Houston F, McCutcheon S, Goldmann W, Chong A, Foster J, Sisó S, González L, Jeffrey M, Hunter N: Prion diseases are efficiently transmitted by blood transfusion in sheep. Blood 2008, 112:4739-4745
-
(2008)
Blood
, vol.112
, pp. 4739-4745
-
-
Houston, F.1
McCutcheon, S.2
Goldmann, W.3
Chong, A.4
Foster, J.5
Sisó, S.6
González, L.7
Jeffrey, M.8
Hunter, N.9
-
26
-
-
0031711879
-
Scrapie infectivity and proteinase K-resistant prion protein in sheep placenta, brain, spleen, and lymph node: Implications for transmission and antemortem diagnosis
-
Race R, Jenny A, Sutton D: Scrapie infectivity and proteinase Kresistant prion protein in sheep placenta, brain, spleen, and lymph node: implications for transmission and antemortem diagnosis. J Infect Dis 1998, 178:949-953 (Pubitemid 28452184)
-
(1998)
Journal of Infectious Diseases
, vol.178
, Issue.4
, pp. 949-953
-
-
Race, R.1
Jenny, A.2
Sutton, D.3
-
27
-
-
0017367439
-
Dangers of accidental person to person transmission of Creutzfeldt Jakob disease by surgery
-
Bernoulli C, Siegfried J, Baumgartner G, Regli F, Rabinowicz T, Gajdusek DC, Gibbs Jr CJ: Danger of accidental person-to-person transmission of Creutzfeldt-Jakob disease by surgery. Lancet 1977, 1: 478-479 (Pubitemid 8045134)
-
(1977)
Lancet
, vol.1
, Issue.8009
, pp. 478-479
-
-
Bernoulli, C.1
Siegfried, J.2
Baumgartner, G.3
-
28
-
-
0026742613
-
Demonstration of the transmissible agent in tissue from a pregnant woman with Creutzfeldt-Jakob disease
-
Tamai Y, Kojima H, Kitajima R, Taguchi F, Ohtani Y, Kawaguchi T, Miura S, Sato M, Ishihara Y: Demonstration of the transmissible agent in tissue from a pregnant woman with Creutzfeldt-Jakob disease. N Engl J Med 1992, 327:649
-
(1992)
N Engl J Med
, vol.327
, pp. 649
-
-
Tamai, Y.1
Kojima, H.2
Kitajima, R.3
Taguchi, F.4
Ohtani, Y.5
Kawaguchi, T.6
Miura, S.7
Sato, M.8
Ishihara, Y.9
-
29
-
-
0028202170
-
Creutzfeldt-Jakob disease in a pregnant woman with an implanted dura mater graft
-
Lane KL, Brown P, Howell DN, Crain BJ, Hulette CM, Burger PC, DeArmond SJ: Creutzfeldt-Jakob disease in a pregnant woman with an implanted dura mater graft. Neurosurgery 1994, 34:737-740 (Pubitemid 24100547)
-
(1994)
Neurosurgery
, vol.34
, Issue.4
, pp. 737-740
-
-
Lane, K.L.1
Brown, P.2
Howell, D.N.3
Crain, B.J.4
Hulette, C.M.5
Burger, P.C.6
Dearmond, S.J.7
Black, P.M.8
Horwitz, N.H.9
-
30
-
-
0034706273
-
The first case of mother-to child transmission of vCJD?
-
Ashraf H: The first case of mother-to child transmission of vCJD? Lancet 2000, 356:1085
-
(2000)
Lancet
, vol.356
, pp. 1085
-
-
Ashraf, H.1
-
31
-
-
0034619085
-
Variant Creutzfeldt-Jakob disease in UK children: A national surveillance study
-
Verity CM, Nicoll A, Will RG, Devereux G, Stellitano L: Variant Creutzfeldt-Jakob disease in UK children: a national surveillance study. Lancet 2000, 356:1224-1227
-
(2000)
Lancet
, vol.356
, pp. 1224-1227
-
-
Verity, C.M.1
Nicoll, A.2
Will, R.G.3
Devereux, G.4
Stellitano, L.5
-
32
-
-
1142273431
-
Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion
-
DOI 10.1016/S0140-6736(04)15486-X
-
Llewelyn CA, Hewitt PE, Knight RS, Amar K, Cousens S, Mackenzie J, Will RG: Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion. Lancet 2004, 363:417-421 (Pubitemid 38210057)
-
(2004)
Lancet
, vol.363
, Issue.9407
, pp. 417-421
-
-
Llewelyn, C.A.1
Hewitt, P.E.2
Knight, R.S.G.3
Amar, K.4
Cousens, S.5
MacKenzie, J.6
Will, R.G.7
-
33
-
-
0141514771
-
Sporadic and familial CJD: Classification and characterisation
-
DOI 10.1093/bmb/66.1.213
-
Gambetti P, Kong Q, Zou WQ, Parchi P, Chen SG: Sporadic and familial CJD: classification and characterisation. Br Med Bull 2003, 66:213-239 (Pubitemid 37173504)
-
(2003)
British Medical Bulletin
, vol.66
, pp. 213-239
-
-
Gambetti, P.1
Kong, Q.2
Zou, W.3
Parchi, P.4
Chen, S.G.5
-
34
-
-
0037197975
-
Sc in placentomes of scrapie-infected sheep
-
DOI 10.1073/pnas.072071199
-
Tuo W, O'Rourke KI, Zhuang D, Cheevers WP, Spraker TR, Knowles DP: Pregnancy status and fetal prion genetics determine PrPSc accumulation in placentomes of scrapie-infected sheep. Proc Natl Acad Sci USA 2002, 99:6310-6315 (Pubitemid 34493308)
-
(2002)
Proceedings of the National Academy of Sciences of the United States of America
, vol.99
, Issue.9
, pp. 6310-6315
-
-
Tuo, W.1
O'Rourke, K.I.2
Zhuang, D.3
Cheevers, W.P.4
Spraker, T.R.5
Knowles, D.P.6
-
35
-
-
0024545093
-
Prion protein biosynthesis in scrapie-infected and uninfected neuroblastoma cells
-
Caughey B, Race RE, Ernst D, Buchmeier MJ, Chesebro B: Prion protein biosynthesis in scrapie-infected and uninfected neuroblastoma cells. J Virol 1989, 63:175-181 (Pubitemid 19028095)
-
(1989)
Journal of Virology
, vol.63
, Issue.1
, pp. 175-181
-
-
Caughey, B.1
Race, R.E.2
Ernst, D.3
Buchmeier, M.J.4
Chesebro, B.5
|