Relationship between nutritional status and pulmonary function in adult cystic fibrosis patients

Journal of Physiology and Pharmacology

Volumn 59, Issue SUPPL. 6, 2008, Pages 253-260

  Gozdzik, J ^a,c   Cofta, S ^a   Piorunek, T ^a   Batura Gabryel, H ^a   Kosicki, J ^b  

^a POZNAN UNIVERSITY OF MEDICAL SCIENCES   (Poland)

^b ADAM MICKIEWICZ UNIVERSITY   (Poland)

^c Department of Pulmonary Diseases ^*  (Poland)

Author keywords

Cystic fibrosis; Lung function; Malnutrition

Indexed keywords

ADULT; ARTICLE; BACTERIAL COLONIZATION; BODY MASS; CLINICAL ARTICLE; CONTROLLED STUDY; CYSTIC FIBROSIS; DISEASE SEVERITY; FEMALE; FORCED EXPIRATORY VOLUME; FUNGUS; HUMAN; LUNG FUNCTION; MALE; MALNUTRITION; NUTRITIONAL STATUS; PRACTICE GUIDELINE; PSEUDOMONAS AERUGINOSA; RISK; STATISTICAL ANALYSIS; LUNG; LUNG FUNCTION TEST; PATHOPHYSIOLOGY; PHYSIOLOGY; SURVIVAL;

ADULT; BODY MASS INDEX; CYSTIC FIBROSIS; FEMALE; FORCED EXPIRATORY VOLUME; HUMANS; LUNG; MALE; MALNUTRITION; NUTRITIONAL STATUS; RESPIRATORY FUNCTION TESTS; SURVIVAL ANALYSIS; YOUNG ADULT;

EID: 64549099797     PISSN: 08675910     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (27)

1. Kerem E, Corey M, Kerem BS et al. The relation between genotype and phenotype in cystic fibrosis - analysis of the most common mutation (AF508). N Eng J Med 1990; 323: 1517-1522.
2. Riordan JR, Rommens JM, Kerem B et al. Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science 1989; 245: 1066-1073. (Erratum, 245: 1437)
3. Rommens JM, Iannuzzi MC, Kerem B et al. Identification of the cystic fibrosis gene: chromosome walking and jumping. Science 1989; 245: 1059-1065.
4. Cystic Fibrosis Mutation Database. CFMDB statistics. http://www.genet. sickkids.on.ca/cftr/. Revised: May 8, 2008.
5. Collins FS. Cystic fibrosis: molecular biology and therapeutic implications. Science 1992; 256:774-779.
6. Elborn JS, Shale DJ, Britton JR. Cystic Fibrosis: current survival and population estimates to the year 2000. Thorax 1991; 46: 881-885.
7. Dankert-Roelse JE, te Meerman GJ. Long term prognosis of patients with cystic fibrosis in relation to early detection by neonatal screening and treatment in a cystic fibrosis centre. Thorax 1995; 50: 712-718
8. Kraemer R, Rudeberg A, Hadorn B et al. Relative underweight in cystic fibrosis and its prognostic value. Acta Paediatr Scand 1978; 67: 33-37.
9. Sinaasappel M, Stern M, Littlewood J et al. Nutrition in patients with cystic fibrosis: a European Consensus. J Cystic Fibrosis 2002; 1: 51-75.
10. Standardized lung function testing. Official statement of the ERS. Eur Respir J Suppl 1993;16; 1-100.
11. Yankaskas JR. Cystic fibrosis adult care: consensus conference report. Chest 2004; 125: 1-39.
12. Pellegrino R, Viegi G, Brusacko V et al. Interpretative strategies for lung function tests. Eur Respir J 2005; 26: 948-968.
13. Zar JH. Biostatistical analysis. 4 Prentice Hall, New Jersey; 1999
14. Sproul A, Huang N. Growth patterns in children with cystic fibrosis. J Pediatr 1993; 122: 1-9.
15. Ramsey BW, Farrell PM, Pencharz PB. Nutritional assessment and management in cystic fibrosis. A Consensus Report. Am J Clin Nutr 1992; 55: 108-116.
16. Dopfer R, Brand P, Müllinger B et al. Inhalation of tobramycin in patients with cystic fibrosis: comparison of two methods. J Physiol Pharmacol 2007; 58 Suppl 5: 141-154.
17. Heijerman HGM ed. 26th Congress European Cystic Fibrosis Society. J Cystic Fibrosis 2003; 2: 4-112.
18. Steinkamp G, Wiedemann B. Relationship between nutritional status and lung function in cystic fibrosis: cross sectional and longitudinal analyses from the German CF quality assurance (CFQA) project. Thorax 2002; 57: 596-601.
19. Cystic Fibrosis Fundation. Cystic Fibrosis Foundation Patient Registry. Annual Data Report 1996. Bethesda, Maryland: Cystic Fibrosis Foundation, 1997.
20. Yankaskas JR. Cystic fibrosis adult care: consensus conference report. Chest 2004; 125: 1-39.
21. Observatoire National de la Mucoviscidose. Rapport sur la situation de la mucoviscidose en France en 2000. Institute National dec Etudes Diographiques. Paris, France 2001.
22. Bell SC, Bowerman AR, Davies CA et al. Nutrition in adults with cystic fibrosis. Clin Nutr 1998; 17: 211-215.
23. White H, Morton AM, Peckham DG, Conway SP. Dietary intakes in adults patients with cystic fibrosis - do they achieve guidelines? J Cystic Fibrosis 2004; 3: 1-7.
24. Pencharz PB, Durie PR. Nutritional management of cystic fibrosis. Annu Rev Nutr 1993; 13: 111-136.
25. Nir M, Lanng H, Johnasen K et al. Long term survival and nutritional data in Danish Centre treated cystic fibrosis patients. Thorax 1996; 51: 1023-1027.
26. Kerem E, Reisman J, Corey M et al. Prediction of mortality in patients with cystic fibrosis. N Engl J Med 1992; 326: 1187-1191.
27. Milla CE, Warwick WJ. Risk of death in cystic fibrosis patients with severely compromised lung function. Chest 1998; 113: 1230-1234.