Codon-specific translational defect caused by a wobble modification deficiency in mutant tRNA from a human mitochondrial disease

Proceedings of the National Academy of Sciences of the United States of America

Volumn 101, Issue 42, 2004, Pages 15070-15075

  Kirino, Yohei ^a   Yasukawa, Takehiro ^a,d   Ohta, Shigeo ^b   Akira, Shigeo ^c   Ishihara, Kaisuke ^c   Watanabe, Kimitsuna ^a,e   Suzuki, Tsutomu ^a  

^a UNIVERSITY OF TOKYO   (Japan)

^b Graduate School of Medicine   (Japan)

^c NIPPON MEDICAL SCHOOL   (Japan)

^d MEDICAL RESEARCH COUNCIL   (United Kingdom)

^e NATIONAL INSTITUTE OF ADVANCED INDUSTRIAL SCIENCE AND TECHNOLOGY AIST   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

5 TAURINOMETHYLURIDINE; ADENINE; CYTOSINE; GUANINE; MITOCHONDRIAL RNA; TAURINE DERIVATIVE; THYMINE; TRANSFER RNA; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; ANTICODON; ARTICLE; CELL LINE; GENE SEQUENCE; HELA CELL; HUMAN; HUMAN CELL; MELAS SYNDROME; POINT MUTATION; PRIORITY JOURNAL; RNA TRANSLATION; SEQUENCE ANALYSIS;

BASE SEQUENCE; BINDING SITES; CELL LINE; CODON; GENETIC ENGINEERING; HUMANS; MELAS SYNDROME; MITOCHONDRIA; MODELS, BIOLOGICAL; MOLECULAR SEQUENCE DATA; NUCLEIC ACID CONFORMATION; POINT MUTATION; PROTEIN BIOSYNTHESIS; RIBOSOMES; RNA, TRANSFER, LEU;

EID: 6344221310     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0405173101     Document Type: Article

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