A cardio-neurological form of laminopathy: Dilated cardiomyopathy with permanent partial atrial standstill and axonal neuropathy

PACE - Pacing and Clinical Electrophysiology

Volumn 32, Issue 3, 2009, Pages 410-415

  Duparc, Alexandre ^a   Cintas, Pascal ^a   Somody, Elisabeth ^b   Bieth, Eric ^c   Richard, Pascale ^d,e   Maury, Philippe ^a   Delay, Marc ^a  

^a CHU RANGUEIL   (France)

^b CH Maillot   (France)

^c CHU PURPAN   (France)

^d Federation de Biochimie   (France)

^e PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

Author keywords

Dilated cardiomyopathy; Laminopathy; Partial atrial standstill

Indexed keywords

DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; DIURETIC AGENT; LAMIN A; LAMIN C; SPIRONOLACTONE;

ADULT; ANAMNESIS; ANGIOCARDIOGRAPHY; ARTICLE; CASE REPORT; CLINICAL FEATURE; CONGESTIVE CARDIOMYOPATHY; DEFIBRILLATOR; DISEASE ASSOCIATION; DRUG MEGADOSE; ELECTROPHYSIOLOGY; GENE EXPRESSION; GENE MUTATION; HEREDITARY MOTOR SENSORY NEUROPATHY; HUMAN; MALE; NEUROPATHY; TRANSESOPHAGEAL ECHOCARDIOGRAPHY; TRANSTHORACIC ECHOCARDIOGRAPHY;

ADULT; ATRIAL FLUTTER; BRADYCARDIA; CARDIOMYOPATHY, DILATED; GENETIC PREDISPOSITION TO DISEASE; HUMANS; LAMIN TYPE A; MALE;

EID: 61449169068     PISSN: 01478389     EISSN: 15408159     Source Type: Journal    
DOI: 10.1111/j.1540-8159.2008.02254.x     Document Type: Article

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