Management of Wilms tumors in Drash and Frasier syndromes

Pediatric Blood and Cancer

Volumn 52, Issue 1, 2009, Pages 55-59

  Auber, F ^a,b   Jeanpierre, C ^c   Denamur, E ^d,e   Jaubert, F ^c   Schleiermacher, G ^f   Patte, C ^g   Cabrol, S ^a   Leverger, G ^a,b   Nihoul Fekete C ^c,e   Sarnacki, S ^c,e  

^a ARMAND TROUSSEAU HOSPITAL   (France)

^b SORBONNE UNIVERSITÉ   (France)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

^d HÔPITAL ROBERT DEBRÉ   (France)

^e UNIVERSITÉ PARIS DESCARTES   (France)

^f INSTITUT CURIE   (France)

^g INSTITUT GUSTAVE ROUSSY   (France)

Author keywords

Denys Drash syndrome; Frasier syndrome; Genetic predisposition to disease; Wilms tumor; WT1 proteins

Indexed keywords

ANTHRACYCLINE; DACTINOMYCIN; IFOSFAMIDE; VINCRISTINE;

ARTICLE; BENIGN TUMOR; BLADDER PAPILLOMA; CANCER CHEMOTHERAPY; CANCER PATIENT; CANCER RADIOTHERAPY; CANCER RISK; CANCER STAGING; CANCER SURVIVOR; CHILD; CLINICAL ARTICLE; DEATH; DENYS DRASH SYNDROME; DIALYSIS; FEMALE; FOLLOW UP; FRASIER SYNDROME; GENE MUTATION; GONADOBLASTOMA; HUMAN; HUMAN TISSUE; KIDNEY FAILURE; MALE; MULTIMODALITY CANCER THERAPY; NEPHROBLASTOMA; NEPHRON SPARING SURGERY; PHENOTYPE; POSTOPERATIVE CARE; PRIORITY JOURNAL; RETROPERITONEAL TUMOR; RETROSPECTIVE STUDY; SOFT TISSUE TUMOR; TRANSITIONAL CELL CARCINOMA; UNINEPHRECTOMY; ADOLESCENT; ADULT; CHRONIC KIDNEY FAILURE; DISEASE MANAGEMENT; NEPHRECTOMY; PRESCHOOL CHILD;

ADOLESCENT; CHILD; CHILD, PRESCHOOL; DENYS-DRASH SYNDROME; DISEASE MANAGEMENT; FRASIER SYNDROME; HUMANS; KIDNEY FAILURE, CHRONIC; NEPHRECTOMY; RETROSPECTIVE STUDIES; WILMS TUMOR; YOUNG ADULT;

EID: 58149394124     PISSN: 15455009     EISSN: 15455017     Source Type: Journal    
DOI: 10.1002/pbc.21759     Document Type: Article

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