Cytoplasmic CUG RNA foci are insufficient to elicit key DM1 features

PLoS ONE

Volumn 3, Issue 12, 2008, Pages

  Dansithong, Warunee ^a   Wolf, Cordula M ^b   Sarkar, Partha ^c   Paul, Sharan ^a   Chiang, Andy ^a   Holt, Ian ^d   Morris, Glenn E ^d   Branco, Dorothy ^b   Sherwood, Megan C ^b   Comai, Lucio ^a   Berul, Charles I ^b   Reddy, Sita ^a  

^a UNIVERSITY OF SOUTHERN CALIFORNIA   (United States)

^b BOSTON CHILDREN S HOSPITAL   (United States)

^c University of Texas Medical Branch School of Medicine   (United States)

^d ROBERT JONES AND AGNES HUNT ORTHOPAEDIC HOSPITAL   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

BETA GALACTOSIDASE; CYTIDINE; CYTOPLASM PROTEIN; GUANOSINE; MESSENGER RNA; MYOTONIC DYSTROPHY PROTEIN KINASE; PROTEIN MBNL1; THYMIDINE; UNCLASSIFIED DRUG; URACIL; CUGBP1 PROTEIN, MOUSE; DNA BINDING PROTEIN; MBNL1 PROTEIN, MOUSE; PROTEIN SERINE THREONINE KINASE; RNA; RNA BINDING PROTEIN;

3' UNTRANSLATED REGION; 5' UNTRANSLATED REGION; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; GENE EXPRESSION; GENE INACTIVATION; HEART DISEASE; HEART MUSCLE CELL; HEART MUSCLE CONDUCTION DISTURBANCE; HUMAN; HUMAN CELL; HUMAN CELL CULTURE; MOUSE; MYOTONIC DYSTROPHY; NONHUMAN; NUCLEOTIDE SEQUENCE; PATHOPHYSIOLOGY; PROTEIN AGGREGATION; PROTEIN LOCALIZATION; RNA ANALYSIS; RNA SPLICING; RNA TRANSPORT; TRINUCLEOTIDE REPEAT; ANIMAL; BIOLOGICAL MODEL; C57BL MOUSE; CELL CULTURE; CELL NUCLEUS; CYTOPLASM; GENETICS; LACTOSE OPERON; MAJOR HISTOCOMPATIBILITY COMPLEX; METABOLISM; PROTEIN BINDING; TRANSGENE; TRANSGENIC MOUSE;

ANIMALIA; BOVINAE; MUS;

ANIMALS; CELL NUCLEUS; CELLS, CULTURED; CYTOPLASM; DNA-BINDING PROTEINS; LAC OPERON; MAJOR HISTOCOMPATIBILITY COMPLEX; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MODELS, BIOLOGICAL; MYOCYTES, CARDIAC; MYOTONIC DYSTROPHY; PROTEIN BINDING; PROTEIN-SERINE-THREONINE KINASES; RNA; RNA-BINDING PROTEINS; TRANSGENES; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 58049101868     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0003968     Document Type: Article

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